Previous chapters have discussed more commonly encountered etiologies of infectious anterior uveitis. On occasion, clinicians encounter rare causative infectious etiologies. The index chapter will address several of these unusual cases. In particular, developed countries seldom encounter parasitic infections that are common in other parts of the world and may provide a diagnostic dilemma requiring surgical specimens for diagnosis. The following chapter will provide two such cases of parasitic anterior uveitis. The chapter will also discuss a case of postoperative toxic anterior segment inflammation and a case of CMV-associated Posner-Schlossman syndrome.