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Nomenclature and Classification of Cardiac Defects

Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care

Abstract

For more in-depth research into congenital cardiac disease, such as for multicentric analysis of outcomes or stratification of risk for interventions, there is need for a uniform and detailed system of nomenclature. The advances in digital technology and communication seen over the last quarter century have facilitated the task of standardization of entry of data and exchange of information.

In this chapter, the authors, as members of the International Society for Nomenclature of Paediatric and Congenital Heart Disease (ISNPCHD), review the principles and challenges of developing a standardized system of nomenclature for congenital heart disease, from the point of view of developing the International Paediatric and Congenital Cardiac Code (IPCCC) and the congenital heart list for the newest iteration of the International Classification of Diseases of the World Health Organization (ICD-11). The authors expand upon certain areas of contention, summarizing some of the discussions that have taken place among those seeking to create a standardized and international system for naming the various lesions encountered in patients presenting with congenital cardiac disease.

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Author information

Authors and Affiliations

  1. Division of Pediatric Cardiology, The Montreal Children’s Hospital of the McGill University Health Centre, 1001 Décarie Blvd, B04.2646, H4A3J1, Montreal, QC, Canada

    M. J. Béland

  2. Paediatric Cardiology Directorate, Royal Brompton & Harefield NHS Trust, Sydney Street, London, SW3 6NP, UK

    R. C. Franklin

  3. Laboratory of Pathology, Heart Institute (InCor), University of Sao Paulo Medical School, Avenida Dr Eneas C Aguiar, 44, CEP 05403-000, Sao Paulo, Brazil

    V. D. Aiello

  4. Hôpital Marie-Lannelongue, 92350, Le Plessis Robinson, France

    L. Houyel

  5. The Children’s Hospital of Philadelphia and Perelman School of Medicine at University of Pennsylvania, 34th Street and Civic Center Blvd, Philadelphia, PA, 19104, USA

    P. M. Weinberg

  6. Institute of Genetic Medicine, Newcastle University, 60 Earlsfield Road, London, SW18 3DN, UK

    R. H. Anderson

Authors
  1. M. J. Béland
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  2. R. C. Franklin
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  3. V. D. Aiello
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  4. L. Houyel
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  5. P. M. Weinberg
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  6. R. H. Anderson
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Corresponding author

Correspondence to M. J. Béland .

Editor information

Editors and Affiliations

  1. Children’s Hospital Colorado University of Colorado Denver, School of, Aurora, Colorado, USA

    Eduardo M. da Cruz

  2. Children's Hospital Colorado University of Colorado School of Medicin, Aurora, Colorado, USA

    Dunbar Ivy

  3. Department of Cardiac Surgery, German Pediatric Heart Center, Sankt Augustin, Germany

    Viktor Hraska

  4. Pediatric Cardiac Surgery, Children's Hospital Colorado University of Colorado, Aurora, Colorado, USA

    James Jaggers

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© 2016 Springer-Verlag London

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Béland, M.J., Franklin, R.C., Aiello, V.D., Houyel, L., Weinberg, P.M., Anderson, R.H. (2016). Nomenclature and Classification of Cardiac Defects. In: da Cruz, E., Ivy, D., Hraska, V., Jaggers, J. (eds) Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care. Springer, London. https://doi.org/10.1007/978-1-4471-4999-6_251-1

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  • DOI: https://doi.org/10.1007/978-1-4471-4999-6_251-1

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  • Publisher Name: Springer, London

  • Online ISBN: 978-1-4471-4999-6

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Chapter history

  1. Latest

    Nomenclature and Classification of Cardiac Defects
    Published:
    11 June 2020

    DOI: https://doi.org/10.1007/978-1-4471-4999-6_251-2

  2. Original

    Nomenclature and Classification of Cardiac Defects
    Published:
    08 August 2016

    DOI: https://doi.org/10.1007/978-1-4471-4999-6_251-1

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