Anomalous pulmonary arteries


The anomalous origin of the pulmonary artery (also called “hemitruncus”) is a rare congenital malformation in which only one pulmonary artery branch, usually the right (opposite to the laterality of the aortic arch), originates from the posterior aspect of the ascending aorta just above the aortic sinotubular junction, without any defect between the ascending aorta and the main pulmonary artery, whereas the main pulmonary artery and the other pulmonary artery branch arise in their normal position and, therefore, are connected with the morphological right ventricle. The other main difference with persistent truncus arteriosus is the presence of two well-separated semilunar valves, aortic and pulmonary valves, and the usual absence of ventricular septal defect. Therefore, hemitruncus defines only the anomalous origin of one pulmonary artery. The anomalous pulmonary artery, most frequently the right, has unrestricted origin, and normal structure, course and distribution.


Pulmonary Artery Aortic Arch Subclavian Artery Ventricular Septal Defect Main Pulmonary Artery 
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  1. Abu-Sulaiman RM, Hashmi A, McCrindle BW, Williams WG, Freedom RM (1998) Anomalous origin of one pulmonary artery from the ascending aorta: 36 years’ experience from one centre. Cardiol Young 8:449–454Google Scholar
  2. Choi BW, Park YH, Choi JY, Choi BI, Kim MJ, Ryu SJ, Lee JK, Sul JH, Lee SK, Cho BK, Choe KO (2001) Using electron beam CT to evaluate conotruncal anomalies in pediatric and adult patients. Am J Roentgenol 177:1045–1049Google Scholar
  3. Dodo H, Alejos JC, Perloff JK, Laks H, Drinkwater DC, Williams RG (1995) Anomalous origin of the left main pulmonary artery from the ascending aorta associated with DiGeorge syndrome. Am J Cardiol 75:1294–1295PubMedCrossRefGoogle Scholar
  4. Fucci C, di Carlo D, di Donato R, Marino B, Calcaterra F, Marcelletti C (1989) Anomalous origin of the right pulmonary artery from the ascending aorta: repair without cardiopulmonary bypass. Int J Cardiol 23:309–313PubMedCrossRefGoogle Scholar
  5. Goo HW, Park IS, Ko JK, Kim YH, Seo DM, Yun TJ, Park JJ, Yoon CH (2003) CT of congenital heart disease: normal anatomy and typical pathologic conditions. Radiographics 23:S147–165PubMedCrossRefGoogle Scholar
  6. Gupta K, Livesay JJ, Lufschanowski R (2001) Absent right pulmonary artery with coronary collaterals supplying the affected lung. Circulation 104:E12–13PubMedCrossRefGoogle Scholar
  7. Livolsi A, Donato L, Kastler B, Willard D, Geisert J (1991) Magnetic resonance imaging in the diagnosis of retrotracheal pulmonary artery. Ann Cardiol Angiol 40:29–32Google Scholar
  8. Mee RBB (1987) Surgical repair of hemitruncus: principles and techniques. J Cardiovasc Surg 2:247–256Google Scholar
  9. Nathan M, Rimmer D, Piercey G, del Nido PJ, Mayer JE (2007) Early repair of hemitruncus: excellent early and late outcomes. J Thorac Cardiovasc Surg 133: 1329–1335PubMedCrossRefGoogle Scholar
  10. Razavi R, Miquel M, Baker E (2004) Diagnosis of hemi-truncus arteriosus by three-dimensional magnetic resonance angiography. Circulation 109:e15–16PubMedCrossRefGoogle Scholar
  11. Rosa U, Wade KC (1987) CT findings in hemitruncus. J Comput Assist Tomogr 11:698–700PubMedCrossRefGoogle Scholar
  12. Sechtem U, Jungehulsing M, de Vivie R, Mennicken U, Hopp HW (1991) Left hemitruncus in adulthood: diagnostic role of magnetic resonance imaging. Eur Heart J 12:1040–1044PubMedGoogle Scholar
  13. Sun AM, Alhabshan F, Branson H, Freedom RM, Yoo SJ (2005) MRI diagnosis of isolated origin of the left subclavian artery from the left pulmonary artery. Pediatr Radiol 35:1259–1262PubMedCrossRefGoogle Scholar
  14. Tsai SK, Chang CI, Wang MJ, Chen SJ, Chiu IS, Chen YS, Lue HC (2001) The assessment of the proximal left pulmonary artery by transoesophageal echocardiography and computed tomography in neonates and infants: a case series. Anesth Analg 93:594–597PubMedCrossRefGoogle Scholar

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