Tricuspid atresia is characterized by the complete absence of a direct communication between the right atrium and the right ventricle (= absent right atrioventricular connection). Tricuspid atresia may range from an imperforate membrane (rarely) to the total absence of the valve with the area replaced by muscular tissue. The floor of the right atrium is completely muscular, frequently with a tiny dimple (= localized fibrous thickening) in the middle, and is totally separated from the ventricular mass by the atrioventricular sulcus (= absent of any potential right atrioventricular connection). The right atrium is generally dilated, and its wall thickened, particularly in the rare (less than 5% of cases) presence of restrictive interatrial communication (generally the interatrial communication is unrestrictive).
KeywordsVentricular Septal Defect Single Ventricle Pulmonary Artery Banding Fontan Circulation Tricuspid Atresia
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