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Dysplasias of Brain Stem and Spinal Cord

  • Reinhard L. Friede

Abstract

Infants afflicted by this uncommon disease exhibit a peculiar facies from birth, characterized by drooping corners of the mouth in association with variable manifestations of ophthalmoplegia. A review of 61 cases by Henderson (1939) showed facial dysplasia in all, abducens palsy in 45, external ophthalmoplegia in 15, ptosis in 6, lingual paresis in 18 and trigeminal paresis in 4; other abnormalities were club foot (19), brachial malformations (13), pectoral muscle defects (8), and mental deficiency (6).

Keywords

Brain Stem Dorsal Horn Club Foot Myelinated Fiber Ventral Horn 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Wien 1975

Authors and Affiliations

  • Reinhard L. Friede
    • 1
    • 2
  1. 1.Case Western Reserve UniversityClevelandUSA
  2. 2.University of ZurichSwitzerland

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