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Retroperitoneale Fibrose (Morbus Ormond)

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Die Urologie

Zusammenfassung

Bei der retroperitonealen Fibrose (RPF, Morbus Ormond) handelt es sich um eine seltene, chronische, entzündlich-fibrosierende Erkrankung des hinteren Bauchraumes. Sie ist gekennzeichnet durch die gutartige Vermehrung von retroperitonealem Weichteilgewebe. In ihrer typischen Lokalisation breitet sich die Fibrose symmetrisch um die Aorta aus, beginnt unterhalb der Nierenstielgefäße und reicht bis unterhalb der Aortenbifurkation. Bei ihrer Ausbreitung erreicht die Fibrose meist als erstes Organ die Ureteren, sodass eine obstruktive Uropathie mit konsekutiver Hydronephrose die häufigste Komplikation dieser Erkrankung ist.

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Correspondence to Alexander Sascha Brandt .

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Brandt, A.S., Goedde, D., Kamper, L., Haage, P., Störkel, S., Roth, S. (2016). Retroperitoneale Fibrose (Morbus Ormond). In: Michel, M., Thüroff, J., Janetschek, G., Wirth, M. (eds) Die Urologie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-39940-4_112

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  • DOI: https://doi.org/10.1007/978-3-642-39940-4_112

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