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Orphan Tracheopathies

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Orphan Lung Diseases

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Abstract

Within the scope of respiratory medicine, central airway diseases have received overall less attention than parenchymal ones. This is perhaps based on the incorrect assumption that disease processes involving the trachea and main bronchi are relatively rare and most often clinically inconsequential. It is also likely secondary to the unfounded belief that severe cases may only be successfully managed by complex and invasive surgical interventions often associated with prohibitive surgical risks in this patient population. Tracheal diseases encompass a variety of disease processes that may be primary or secondary to underlying systemic diseases, whether inflammatory, infectious or neoplastic in nature. Central airway diseases can generally be successfully managed by a variety of endoscopic procedures, which within this past decade have grown exponentially in number and complexity. In that regard, central airway diseases present unique challenges and opportunities for respiratory physicians and can be largely credited for the development of the subspecialty of Interventional Pulmonary Medicine.

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Authors and Affiliations

  1. Division of Pulmonary and Critical Care Medicine, Mayo Clinic College of Medicine, Gonda 18 South, Mayo Clinic, 200 First St. SW, Rochester, MN, 55905, USA

    Fabien Maldonado MD & Jay H. Ryu MD

  2. Department of Diseases of the Thorax, Interventional Pulmonology Unit, GB Morgagni Hospital, Forli, Italy

    Sara Tomassetti MD

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  1. Fabien Maldonado MD
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  2. Sara Tomassetti MD
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  3. Jay H. Ryu MD
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Correspondence to Fabien Maldonado MD .

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Editors and Affiliations

  1. Rare Pulmonary Diseases, Hôpital Louis Pradel, Lyon, France

    Vincent Cottin

  2. Rare Pulmonary Diseases, Hôpital Louis Pradel, Lyon, France

    Jean-Francois Cordier

  3. Respiratory Medicine, University of Southampton, Southampton, United Kingdom

    Luca Richeldi

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Maldonado, F., Tomassetti, S., Ryu, J.H. (2015). Orphan Tracheopathies. In: Cottin, V., Cordier, JF., Richeldi, L. (eds) Orphan Lung Diseases. Springer, London. https://doi.org/10.1007/978-1-4471-2401-6_6

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