Autoimmune Retinopathy

  • Karen R. Armbrust
  • Maggie M. Wei
  • Brett G. Jeffrey
  • H. Nida Sen
Living reference work entry


Non-paraneoplastic autoimmune retinopathy (AIR) typically presents in middle-aged females with vision loss, visual field loss, electroretinography (ERG) changes, and positive anti-retinal antibody testing, often in the context of an unremarkable fundus examination. Fundus autofluorescence (FAF) and optical coherence tomography (OCT) may be helpful ancillary tests in AIR. Evaluation for underlying malignancy with the patient’s primary care provider is essential to rule out a paraneoplastic retinopathy.


Optical Coherence Tomography Visual Field Loss Photoreceptor Layer Fundus Autofluorescence Ellipsoid Zone 
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Suggested Reading

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Copyright information

© Springer India (outside the USA) 2016

Authors and Affiliations

  • Karen R. Armbrust
    • 1
  • Maggie M. Wei
    • 1
  • Brett G. Jeffrey
    • 2
  • H. Nida Sen
    • 1
  1. 1.Laboratory of ImmunologyNational Eye Institute, National Institutes of HealthBethesdaUSA
  2. 2.Ophthalmic Genetics and Visual Function BranchNational Eye Institute, National Institutes of HealthBethesdaUSA

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