Zusammenfassung
Alle cholestatischen Erkrankungen des Neugeborenen gehören zu den jeweils seltenen Krankheiten in dieser Altersgruppe und bedürfen nur in wenigen Fällen einer unmittelbaren chirurgischen Therapie. Trotzdem repräsentieren diese Patienten die größte Gruppe der Lebertransplantationen im Kindesalter. Der Stellenwert der chirurgischen Erstbehandlung darf dennoch nicht unterschätzt werden, da diese gerade bei seltenen Erkrankungen für den weiteren Verlauf entscheidend sein kann. Das gilt z. B. für die Überlebenszeit mit der eigenen Leber bei der Gallengangatresie oder für einen symptomfreien Langzeitverlauf nach Resektionen von Choledochuszysten.
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Petersen, C. (2018). Erkrankungen der Leber und Gallenwege bei Kindern und Jugendlichen. In: von Schweinitz, D., Ure, B. (eds) Kinderchirurgie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-53390-1_59-1
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