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Erkrankungen der Leber und Gallenwege bei Kindern und Jugendlichen

  • Claus Petersen
Living reference work entry
Part of the Springer Reference Medizin book series (SRM)

Zusammenfassung

Alle cholestatischen Erkrankungen des Neugeborenen gehören zu den jeweils seltenen Krankheiten in dieser Altersgruppe und bedürfen nur in wenigen Fällen einer unmittelbaren chirurgischen Therapie. Trotzdem repräsentieren diese Patienten die größte Gruppe der Lebertransplantationen im Kindesalter. Der Stellenwert der chirurgischen Erstbehandlung darf dennoch nicht unterschätzt werden, da diese gerade bei seltenen Erkrankungen für den weiteren Verlauf entscheidend sein kann. Das gilt z. B. für die Überlebenszeit mit der eigenen Leber bei der Gallengangatresie oder für einen symptomfreien Langzeitverlauf nach Resektionen von Choledochuszysten.

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Copyright information

© © Springer-Verlag GmbH Deutschland 2018

Authors and Affiliations

  1. 1.Kinderchirurgische KlinikMedizinische Hochschule HannoverHannoverDeutschland

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