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Ichthyosen

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Braun-Falco's Dermatologie, Venerologie und Allergologie

Part of the book series: Springer Reference Medizin ((SRM))

Zusammenfassung

Hereditäre Ichthyosen sind erbliche Verhornungsstörungen, die sich auf die gesamte Haut beziehen und durch Verdickung der Hornhaut und Schuppung gekennzeichnet sind. Pathophysiologisch gesehen handelt es sich primär um Störungen der epidermalen Barriere. Die Vielzahl der äußerst seltenen Erkrankungen zu überblicken, ist eine Herausforderung: Die Klassifikation erfolgt auf klinisch-genetischer Basis und nach nichtsyndromalen oder syndromalen Formen. Die diagnostische Abgrenzung der Ichthyosis vulgaris und der X-chromosomal-rezessiven Ichthyose von den seltenen kongenitalen Ichthyosen ist von großer praktischer Bedeutung. Zu unterscheiden sind zudem erworbene ichthyosiforme Hautzustände. In diesem Kapitel werden die faszinierenden einzelnen genetischen Störungen erklärt. Zur Schärfung des klinischen Blicks ist es mit ausführlichem Bildmaterial unterlegt. Die Therapiehinweise folgen der Maxime, dass mittels symptomatischer Therapiemaßnahmen viel für die Patienten erreicht werden kann.

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Authors and Affiliations

  1. Klinik und Poliklinik für Hautkrankheiten, Universitätsklinikum Münster, Von-Esmarch-Str. 58, 48151, Münster, Deutschland

    Vinzenz Oji

  2. Hautarztpraxis am Buddenturm, Rudolf-von-Langen-Str. 55, 48147, Münster, Deutschland

    Vinzenz Oji

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  1. Vinzenz Oji
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Correspondence to Vinzenz Oji .

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Editors and Affiliations

  1. Dermatologie und Allergologie, Universitätsklinikum München Klinik und Poliklinik für, München, Bayern, Germany

    Gerd Plewig

  2. Dermatologie und Allergologie, Universitätsklinikum München Klinik und Poliklinik für, München, Bayern, Germany

    Thomas Ruzicka

  3. J.W.Goethe-Universität, Klinik für Dermatologie, Venerologie und Allergologie, Frankfurt, Hessen, Germany

    Roland Kaufmann

  4. Univ.Klinikum Marburg Klinik für Dermatologie und Allergologie, Marburg, Germany

    Michael Hertl

Section Editor information

  1. Klinik für Dermatologie und Allergologie, Universitätsklinikum Marburg, Baldingerstr.1, 35043, Marburg, Deutschland

    Michael Hertl

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Oji, V. (2018). Ichthyosen. In: Plewig, G., Ruzicka, T., Kaufmann, R., Hertl, M. (eds) Braun-Falco's Dermatologie, Venerologie und Allergologie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-49546-9_60-1

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  • DOI: https://doi.org/10.1007/978-3-662-49546-9_60-1

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