Zusammenfassung
Die tumorassoziierten Genodermatosen sind extrem seltene autosomal-dominant erbliche Erkrankungen, die durch typische Hauterscheinungen charakterisiert sind und zur Entstehung maligner Tumoren verschiedener Organe disponieren. Die diagnostische Einordnung der häufig vorangehenden Hauterscheinungen ermöglicht daher die Identifizierung von Patienten mit einem angeborenen Risiko für die Entwicklung spezifischer Krebserkrankungen und liefert somit einen wichtigen Beitrag zur Krebsprävention.
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Berneburg, M., Kruse, R. (2018). Tumorassoziierte Genodermatosen. In: Plewig, G., Ruzicka, T., Kaufmann, R., Hertl, M. (eds) Braun-Falco's Dermatologie, Venerologie und Allergologie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-49546-9_114-1
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