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Autoimmunpankreatitis

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DGIM Innere Medizin

Part of the book series: Springer Reference Medizin ((SRM))

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Zusammenfassung

Die Autoimmunpankreatitis ist eine verhältnismäßig seltene, eigenständige Pankreaserkrankung, die sich durch diffuse oder fokale Pankreasentzündung, lymphoplasmazelluläres Infiltrat mit Fibrosierung und Ansprechen auf Steroide auszeichnet. Die Autoimmunpankreatitis vom Typ 1 ist die pankreatische Manifestation der systemischen IgG4-assoziierten Erkrankung. Bei der Autoimmunpankreatitis vom Typ 2 handelt es sich um eine isolierte Erkrankung des Pankreas, die in erhöhtem Maße mit chronisch-entzündlichen Darmerkrankungen vergesellschaftet ist. Für die Autoimmunpankreatitis sind einheitliche internationale Konsensus-Diagnosekriterien veröffentlicht worden. Die wichtigsten Differenzialdiagnosen sind maligne Tumoren des Pankreas und der unteren Gallenwege. Die Gabe von Steroiden ist bei allen Patienten mit Nachweis oder hochgradigem Verdacht auf eine Autoimmunpankreatitis indiziert.

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Authors and Affiliations

  1. Klinik für Innere Medizin A der Universitätsmedizin Greifswald, Ferdinand-Sauerbruch-Straße, 17475, Greifswald, Deutschland

    Georg Beyer, Julia Mayerle & Markus M. Lerch

Authors
  1. Georg Beyer
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  2. Julia Mayerle
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  3. Markus M. Lerch
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Corresponding author

Correspondence to Markus M. Lerch .

Editor information

Editors and Affiliations

  1. Medizinische Klinik I, Universitätsklinikum Schleswig-Hoslstein, Campus Lübeck, Lübeck, Schleswig-Holstein, Germany

    Hendrik Lehnert

  2. TU Dresden Universitätsklinikum Carl Gustav Carus, Dresden, Germany

    Sebastian M. Schellong

  3. FB Gastroenterologie und Hepatologie, Universitätsklinikum Leipzig Medizinische Klinik und Poliklinik II, Leipzig, Sachsen, Germany

    Joachim Mössner

  4. Krankenhaus Barmherzige Brüder, Regensburg, Germany

    Cornel C. Sieber

  5. Nürnberg, Bayern, Germany

    Walter Swoboda

  6. Universitätsklinikum Giessen und Marburg Klinik für Innere Medizin, Marburg, Hessen, Germany

    Andreas Neubauer

  7. Interdisziplinärer Schwerpunkt für Hämos, Universitätsklinikum Gießen und Marburg, Gießen, Germany

    Bettina Kemkes-Matthes

  8. Klinik für Gastroenterologie,Hepatologie, Medizinische Hochschule Hannover, Hannover, Germany

    Michael P. Manns

  9. Sektion für Molekulare und Klinische Inf, Universitätsklinikum Schleswig-Holstein,, Lübeck, Germany

    Jan Rupp

  10. Abt. Kardiologie und Pneumologie, Universitätsklinikum Göttingen Herzzentrum Göttingen, Göttingen, Germany

    Gerd Hasenfuß

  11. Abt. Nephrologie und Klinische Immunologie, Univ.Klinikum Aachen Medizinische Klinik II, Aachen, Germany

    J. Floege

  12. Universitätsklinikum Köln Klinik I für Innere Medizin, Köln, Germany

    Michael Hallek

  13. Klinik für Pneumologie, Medizinische Hochschule Hannover (MHH) Zentrum Innere Medizin, Hannover, Germany

    Tobias Welte

  14. Klinik u. Poliklinik für Innere Medizin, Universitätsmedizin Greifswald, Greifswald, Germany

    Markus Lerch

  15. Dr.-Horst-Schmidt-Kliniken GmbH, Wiesbaden, Germany

    Elisabeth Märker-Hermann

  16. Klinische Toxikologie, Giftinformation, Universitätsklinikum Mainz II. Medizinische Klinik und Poliklinik, Mainz, Germany

    Ludwig Sacha Weilemann

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Beyer, G., Mayerle, J., Lerch, M.M. (2015). Autoimmunpankreatitis. In: Lehnert, H., et al. DGIM Innere Medizin. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-54676-1_98-1

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  • DOI: https://doi.org/10.1007/978-3-642-54676-1_98-1

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