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Pädiatrie pp 1–9Cite as

Episodische Fiebersyndrome – autoinflammatorische Syndrome

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Part of the book series: Springer Reference Medizin ((SRM))

Zusammenfassung

Autoinflammatorische Syndrome sind seltene, in der Regel monogen erbliche chronische Erkrankungen, gekennzeichnet durch multisystemische Entzündungsprozesse mit rekurrierenden Fieberattacken (Tab. 1). Charakteristische Autoimmunphänomene wie Autoantikörper oder autoantigenspezifische T-Zellen werden nicht nachgewiesen.

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Authors and Affiliations

  1. Asklepios Klinik Sankt Augustin GmbH, Zentrum Allgemeine Pädiatrie und Neonatologie, Arnold-Janssen-Str. 29, 53757, Sankt Augustin, Deutschland

    G. Horneff

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  1. G. Horneff
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Correspondence to G. Horneff .

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Editors and Affiliations

  1. Universität Heidelberg, Zentrum für Kinder- und Jugendmedizin, Heidelberg, Germany

    Georg F. Hoffmann

  2. Zentrum für Kinderheilkunde, Bonn, Germany

    Michael J. Lentze

  3. Sinzheim, Germany

    Jürgen Spranger

  4. Universitätsmedizin Mainz Zentrum für Kinder- und Jugendmediz, Mainz, Germany

    Fred Zepp

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Horneff, G. (2015). Episodische Fiebersyndrome – autoinflammatorische Syndrome. In: Hoffmann, G., Lentze, M., Spranger, J., Zepp, F. (eds) Pädiatrie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-54671-6_107-1

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  • DOI: https://doi.org/10.1007/978-3-642-54671-6_107-1

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  • Online ISBN: 978-3-642-54671-6

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Chapter history

  1. Latest

    Episodische Fiebersyndrome – autoinflammatorische Syndrome
    Published:
    22 August 2019

    DOI: https://doi.org/10.1007/978-3-642-54671-6_107-2

  2. Original

    Episodische Fiebersyndrome – autoinflammatorische Syndrome
    Published:
    31 March 2015

    DOI: https://doi.org/10.1007/978-3-642-54671-6_107-1

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