Malignant Small Cell Tumor of Thoracopulmonary Region/Primitive Neuroectodermal Tumor/Askin Tumor, Pleural
Reference work entry
Askin-Rosai tumor; Askin tumor; Peripheral neuroepithelioma of the thoracopulmonary region; Pleural malignant small cell tumor of the thoracopulmonary region; Primitive neuroectodermal tumor
Primitive neuroectodermal tumors (PNETs) of the thoracopulmonary region carry the specific name of Askin tumor. They are a group of highly aggressive malignant tumors involving the bones and soft tissue and are characterized by the presence of undifferentiated small round blue cells of neuroectodermal origin (Figs. 1 and 2).
References and Further Reading
- Folpe, A. L., Hill, C. E., Parham, D. M., O’Shea, P. A., & Weiss, S. W. (2000). Immunohistochemical detection of FLI-1 protein expression a study of 132 round cell tumors with emphasis on CD99-positive mimics of Ewing’s sarcoma/primitive neuroectodermal tumor. American Journal of Surgical Pathology, 24(12), 1657–1662.PubMedCrossRefGoogle Scholar
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