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Pediatric Hydrocephalus pp 1–29Cite as

Cerebrospinal Fluid hydrodynamics in Craniosynostosis

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Abstract

Hydrocephalus presents specific challenges – in both diagnosis and management – in patients with craniosynostosis. Hydrocephalus has been recognized as a feature of the syndromic forms, in particular the more phenotypically severe, for a long time. Controversy still exists regarding the pathophysiology, prevalence, and optimal management strategy of hydrocephalus in children affected by syndromic craniosynostosis. In this chapter, we review the literature and our experience regarding each of these important facets, with an attempt made to offer some unifying theories and practical guides to management. In addition, we will review specific considerations, including the association of hydrocephalus, craniosynostosis, and Chiari 1, as well as the use of craniofacial surgery for skull deformity induced either by hydrocephalus itself or its treatment.

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Authors and Affiliations

  1. Department of Neurosurgery, Great Ormond Street Hospital, London, UK

    Gregory James & Dominic N. P. Thompson

  2. Developmental Neurosciences Programme, Great Ormond Street Institute of Child Health, University College London, London, UK

    Gregory James & Dominic N. P. Thompson

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  1. Gregory James
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  2. Dominic N. P. Thompson
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Correspondence to Gregory James .

Editor information

Editors and Affiliations

  1. Pediatric Neurosurgery, Santobono Pausilipon Children’s Hospital, Naples, Italy

    Giuseppe Cinalli

  2. Division of Pediatric Neurosurgery, Acıbadem University, School of Medicine, Istanbul, Istanbul, Turkey

    M. Memet Ozek

  3. Hopital Necker-Enfants Malades, Paris, France

    Christian Sainte-Rose

Section Editor information

  1. Department of Pediatric Neurosurgery, Santobono-Pausilipon Children’s Hospital, Naples, Italy

    Giuseppe Cinalli

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James, G., Thompson, D.N. (2018). Cerebrospinal Fluid hydrodynamics in Craniosynostosis. In: Cinalli, G., Ozek, M., Sainte-Rose, C. (eds) Pediatric Hydrocephalus. Springer, Cham. https://doi.org/10.1007/978-3-319-31889-9_64-1

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  • DOI: https://doi.org/10.1007/978-3-319-31889-9_64-1

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  • Print ISBN: 978-3-319-31889-9

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