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Scoliosis and Other Congenital Vertebral Anomalies

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Book cover Textbook of Pediatric Neurosurgery

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Abstract

Congenital vertebral malformations with scoliosis result from embryological defects in vertebral element formation or segmentation. Etiologies include genetic causes as well as environmental factors. Patients have an increased incidence of associated anomalies that involve cardiac, genitourinary, and neurological systems. Clinical significance of curve progression depends on the age at diagnosis, location of the curve, and the nature of the underlying vertebral malformation. Surgical intervention may be appropriate in younger patients with thoracolumbar deformities and specific vertebral anomalies. Surgical options include convex hemiepiphysiodesis, instrumented fusion, osteotomies and vertebrectomies, as well as growing systems. This chapter will discuss diagnosis, workup, and treatment strategies for congenital scoliosis.

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Author information

Authors and Affiliations

  1. Department of Neurological Surgery, Johns Hopkins Medicine, Baltimore, MD, USA

    Mari L. Groves

  2. Shriners Hospitals for Children-Philadelphia, 3551 N Broad St, Philadelphia, PA, 19140, USA

    Andrew C. Vivas & Amer F. Samdani

Authors
  1. Mari L. Groves
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  2. Andrew C. Vivas
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  3. Amer F. Samdani
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Corresponding author

Correspondence to Amer F. Samdani .

Editor information

Editors and Affiliations

  1. International Neuroscience Institute, Hannover, Germany

    Concezio Di Rocco

  2. Oakland Medical Center, Oakland, California, USA

    Dachling Pang

  3. University of Toronto Hospital for Sick Children, Toronto, Ontario, Canada

    James T. Rutka

Section Editor information

  1. Davis; and Kaiser Permanente Hospitals of Northern California, University of California, Oakland, United States of America

    Dachling Pang

  2. Seoul National University, Seoul, Republic of Korea

    Kyu-Chang Wang

  3. Institute of Child Health, University College London, London, UK

    Dominic Thompson

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Groves, M.L., Vivas, A.C., Samdani, A.F. (2017). Scoliosis and Other Congenital Vertebral Anomalies. In: Di Rocco, C., Pang, D., Rutka, J. (eds) Textbook of Pediatric Neurosurgery. Springer, Cham. https://doi.org/10.1007/978-3-319-31512-6_122-1

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  • DOI: https://doi.org/10.1007/978-3-319-31512-6_122-1

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  • Print ISBN: 978-3-319-31512-6

  • Online ISBN: 978-3-319-31512-6

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