Skip to main content
SpringerLink
Log in

Dermatomyositis

  • Reference work entry
  • First Online:
Dermatopathology

Part of the book series: Encyclopedia of Pathology ((EP))

  • 1529 Accesses

Synonyms

Lilac disease; Polymyositis with skin involvement

Definition

Dermatomyositis is a connective tissue disease characterized by inflammatory and degenerative changes of the muscles and skin. Dermatomyositis is one of the idiopathic inflammatory myopathies, a group of acquired skeletal muscle diseases that includes five subsets: classic or adult dermatomyositis (DM), polymyositis (PM), myositis with malignancy, juvenile dermatomyositis/polymyositis, and myositis overlapping with another collagen vascular disorder. Another subset called amyopathic dermatomyositis (ADM) or dermatomyositis sine myositis presenting with only skin involvement for at least 2 years since the diagnosis has been recently recognized. Although there is some overlap, these subsets are indeed heterogeneous both in terms of presentation and pathophysiology. Cutaneous involvement is the primary clinical feature distinguishing patients with DM from those with PM, and it may precede, accompany, or follow the...

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Log in via an institution
Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 299.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Hardcover Book
USD 449.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

References and Further Reading

  • Callen, J. P., & Wortmann, R. L. (2006). Dermatomyositis. Clinics in Dermatology, 24, 363–373.

    Article  PubMed  Google Scholar 

  • Krathen, M. S., Fiorentino, D., & Werth, V. P. (2008). Dermatomyositis. Current Directions in Autoimmunity, 10, 313–332.

    Article  CAS  PubMed  PubMed Central  Google Scholar 

  • Magro, C. M., Segal, J. P., Crowson, A. N., & Chadwick, P. (2010). The phenotypic profile of dermatomyositis and lupus erythematosus: A comparative analysis. Journal of Cutaneous Pathology, 37, 659–671.

    Article  PubMed  Google Scholar 

  • Mammen, A. L. (2010). Dermatomyositis and polymyositis: Clinical presentation, autoantibodies, and pathogenesis. Annals of the New York Academy of Sciences, 1184, 134–153.

    Article  CAS  PubMed  Google Scholar 

  • Smith, E. S., Hallman, J. R., DeLuca, A. M., Goldenberg, G., Jorizzo, J. L., & Sangueza, O. P. (2009). Dermatomyositis: A clinicopathological study of 40 patients. American Journal of Dermatopathology, 31, 61–67.

    Article  PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Section of Dermatology, Department of Health Sciences (DISSAL) and Unity of Pathology, University of Genova, Viale Benedetto XV, 7, 16132, Genova, Italy

    Franco Rongioletti

  2. Section of Dermatology, Department of Health Sciences and Unity of Pathology, University of Genova, Viale Benedetto XV, 7, 16132, Genova, Italy

    Martina Montinari

Authors
  1. Franco Rongioletti
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. Martina Montinari
    View author publications

    You can also search for this author in PubMed Google Scholar

Corresponding author

Correspondence to Franco Rongioletti .

Editor information

Editors and Affiliations

  1. Division of Pathological Anatomy, Department of Surgery and Translational Medicine, University of Florence, School of Human Health Sciences, Florence, Italy

    Daniela Massi

Rights and permissions

Reprints and permissions

Copyright information

© 2016 Springer International Publishing Switzerland

About this entry

Cite this entry

Rongioletti, F., Montinari, M. (2016). Dermatomyositis. In: Massi, D. (eds) Dermatopathology. Encyclopedia of Pathology. Springer, Cham. https://doi.org/10.1007/978-3-319-30006-1_413

Download citation

  • DOI: https://doi.org/10.1007/978-3-319-30006-1_413

  • Published:

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-30005-4

  • Online ISBN: 978-3-319-30006-1

  • eBook Packages: MedicineReference Module Medicine

Publish with us

Policies and ethics

Search

Navigation