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Clear Cell Carcinomas of the Bile Ducts

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Tumors and Tumor-Like Lesions of the Hepatobiliary Tract

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Abstract

Similar to clear cell hepatocellular carcinoma, rare variants of cholangiocarcinoma are characterized by clear cells that resemble cells of metastasizing renal cell carcinomas. Clear cell cholangiocarcinoma with a glandular or acinar pattern develops in extrahepatic bile ducts and in the gallbladder, but very rare forms have also been observed within the liver, whereby intrahepatic clear cell cholangiocarcinomas were usually small and peripheral lesions. These neoplasms exhibit a stromal reaction (desmoplasia) similar to that of classical cholangiocarcinomas. A very rare subset of clear cell cholangiocarcinoma shows a papillary component (clear cell papillary carcinoma of the liver).

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Authors and Affiliations

  1. University of Bern, Bern, Switzerland

    Arthur Zimmermann

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  1. Arthur Zimmermann
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Correspondence to Arthur Zimmermann .

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Zimmermann, A. (2017). Clear Cell Carcinomas of the Bile Ducts. In: Tumors and Tumor-Like Lesions of the Hepatobiliary Tract. Springer, Cham. https://doi.org/10.1007/978-3-319-26956-6_37

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  • DOI: https://doi.org/10.1007/978-3-319-26956-6_37

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-26954-2

  • Online ISBN: 978-3-319-26956-6

  • eBook Packages: MedicineReference Module Medicine

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