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Pediatric and Adolescent Cholangiocarcinoma and Related Lesions

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Tumors and Tumor-Like Lesions of the Hepatobiliary Tract

Abstract

Bile duct cancers similar to those of adult patients also develop in the pediatric age group, but pediatric cholangiocarcinoma is a very rare condition in infants and children. The neoplasms become slightly more common in adolescents. Pediatric cholangiocarcinoma is usually associated with congenital hepatobiliary disorders, including congenital biliary dilatation and choledochal cysts, congenital pancreaticobiliary maljunction, and congenital biliary atresia. Cholangiocarcinoma can also develop in individuals who suffered from primary sclerosing cholangitis in childhood and in adolescents following pediatric-onset inflammatory bowel disease.

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Authors and Affiliations

  1. University of Bern, Bern, Switzerland

    Arthur Zimmermann

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  1. Arthur Zimmermann
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Correspondence to Arthur Zimmermann .

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Zimmermann, A. (2017). Pediatric and Adolescent Cholangiocarcinoma and Related Lesions. In: Tumors and Tumor-Like Lesions of the Hepatobiliary Tract. Springer, Cham. https://doi.org/10.1007/978-3-319-26956-6_32

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  • DOI: https://doi.org/10.1007/978-3-319-26956-6_32

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-26954-2

  • Online ISBN: 978-3-319-26956-6

  • eBook Packages: MedicineReference Module Medicine

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