Synonyms
Extracardiac rhabdomyoma; Rhabdomyoma of genital parts
Definition
Rare benign mesenchymal tumours with skeletal muscle differentiation
Clinical Features
Incidence
Extracardiac rhabdomyomas are very rare neoplasm, comprising less than 2% of the neoplasm of the skeletal muscle origin. Because of their extreme rarity, the incidence of genital rhabdomyomas is unknown.
Age
In males, the average age is lower than in women, affecting mainly adolescents and infants.
Sex
Only rare cases have been reported in males.
Site
The most commonly affected sites are the epididymis, spermatic cord, tunica vaginalis, or paratesticular regions. One prostatic rhabdomyoma is also reported.
Treatment
Surgical intervention with complete excision is normally curative. Radiation therapy and chemotherapy are not usually required.
Outcome
The prognosis is excellent with surgical intervention and completes removal of the lesion, even though the tumors may be deep seated. Recurrences are reported only after...
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Han, Y., Qiu, X. S., Li, Q. C., et al. (2012). Epididymis rhabdomyoma: A case report and literature review. Diagnostic Pathology, 7, 47.
Jo, V. Y., Reith, J. D., Coindre, J. M., & Fletcher, C. D. (2013). Paratesticular rhabdomyoma: A morphologically distinct sclerosing variant. The American Journal of Surgical Pathology, 37(11), 1737–1742.
Tanda, F., Rocca, P. C., Bosincu, L., Massarelli, G., Cossu, A., & Manca, A. (1997). Rhabdomyoma of the tunica vaginalis of the testis: A histologic, immunohistochemical, and ultrastructural study. Modern Pathology, 10, 608–611.
Wehner, M. S., Humphreys, J. L., & Sharkey, F. E. (2000). Epididymal rhabdomyoma: Report of a case, including histologic and immunohistochemical findings. Archives of Pathology & Laboratory Medicine, 124, 1518–1519.
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Gaeta, R., Franchi, A. (2020). Rhabdomyoma. In: Raspollini, M.R., Lopez-Beltran, A. (eds) Uropathology. Encyclopedia of Pathology. Springer, Cham. https://doi.org/10.1007/978-3-030-41894-6_4930
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DOI: https://doi.org/10.1007/978-3-030-41894-6_4930
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Publisher Name: Springer, Cham
Print ISBN: 978-3-030-41893-9
Online ISBN: 978-3-030-41894-6
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