Uropathology

2020 Edition
| Editors: Maria Rosaria Raspollini, Antonio Lopez-Beltran

Rhabdomyoma

  • Raffaele Gaeta
  • Alessandro FranchiEmail author
Reference work entry
DOI: https://doi.org/10.1007/978-3-030-41894-6_4930
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Synonyms

Extracardiac rhabdomyoma; Rhabdomyoma of genital parts

Definition

Rare benign mesenchymal tumours with skeletal muscle differentiation

Clinical Features

  • Incidence

    Extracardiac rhabdomyomas are very rare neoplasm, comprising less than 2% of the neoplasm of the skeletal muscle origin. Because of their extreme rarity, the incidence of genital rhabdomyomas is unknown.

  • Age

    In males, the average age is lower than in women, affecting mainly adolescents and infants.

  • Sex

    Only rare cases have been reported in males.

  • Site

    The most commonly affected sites are the epididymis, spermatic cord, tunica vaginalis, or paratesticular regions. One prostatic rhabdomyoma is also reported.

  • Treatment

    Surgical intervention with complete excision is normally curative. Radiation therapy and chemotherapy are not usually required.

  • Outcome

    The prognosis is excellent with surgical intervention and completes removal of the lesion, even though the tumors may be deep seated. Recurrences are reported only after...

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References

  1. Han, Y., Qiu, X. S., Li, Q. C., et al. (2012). Epididymis rhabdomyoma: A case report and literature review. Diagnostic Pathology, 7, 47.PubMedPubMedCentralCrossRefGoogle Scholar
  2. Jo, V. Y., Reith, J. D., Coindre, J. M., & Fletcher, C. D. (2013). Paratesticular rhabdomyoma: A morphologically distinct sclerosing variant. The American Journal of Surgical Pathology, 37(11), 1737–1742.PubMedCrossRefGoogle Scholar
  3. Tanda, F., Rocca, P. C., Bosincu, L., Massarelli, G., Cossu, A., & Manca, A. (1997). Rhabdomyoma of the tunica vaginalis of the testis: A histologic, immunohistochemical, and ultrastructural study. Modern Pathology, 10, 608–611.PubMedGoogle Scholar
  4. Wehner, M. S., Humphreys, J. L., & Sharkey, F. E. (2000). Epididymal rhabdomyoma: Report of a case, including histologic and immunohistochemical findings. Archives of Pathology & Laboratory Medicine, 124, 1518–1519.Google Scholar

Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  1. 1.Department of Translational Research and of New Technologies in Medicine and SurgeryUniversity of PisaPisaItaly