Von Hippel-Lindau Disease

Living reference work entry


Von Hippel-Lindau disease (VHL) is a rare hereditary cancer syndrome. The prevalence is estimated at 1 in 85,000 with an incidence of 1 in 45,500 live births (Friedrich 2001).


Renal Cell Carcinoma Preimplantation Genetic Diagnosis Clear Cell Renal Cell Carcinoma Pancreatic Neuroendocrine Tumor Malignant Pheochromocytoma 
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Copyright information

© Springer Science+Business Media LLC 2016

Authors and Affiliations

  1. 1.Medical GeneticsShriners Hospitals for ChildrenShreveportUSA
  2. 2.Perinatal and Clinical Genetics, Department of PediatricsLSU Health Sciences CenterShreveportUSA

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