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Von Hippel-Lindau Disease

Living reference work entry

Abstract

Von Hippel-Lindau disease (VHL) is a rare hereditary cancer syndrome. The prevalence is estimated at 1 in 85,000 with an incidence of 1 in 45,500 live births (Friedrich 2001).

Keywords

Renal Cell Carcinoma Preimplantation Genetic Diagnosis Clear Cell Renal Cell Carcinoma Pancreatic Neuroendocrine Tumor Malignant Pheochromocytoma 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media LLC 2016

Authors and Affiliations

  1. 1.Medical GeneticsShriners Hospitals for ChildrenShreveportUSA
  2. 2.Perinatal and Clinical Genetics, Department of PediatricsLSU Health Sciences CenterShreveportUSA

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