Pachyonychia congenita (PC) is a group of rare genetically inherited diseases characterized by nail dystrophy and by varying features of ectodermal dysplasias. There are two major clinical subtypes recognized: type I with oral leukokeratosis and type II with multiple pilosebaceous cysts (Çelebi et al. 1999).
KeywordsBrittle Sponge Candida Cataract Gabapentin
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