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Aortopulmonary Window

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Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care

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Abstract

Aortopulmonary window is a rare defect caused by failure of fusion of the two opposing conotruncal ridges that are responsible for separating the truncus arteriosus into the aorta and pulmonary artery. Aortopulmonary window may occur as an isolated lesion, or it can be associated with other cardiac abnormalities in a third to one-half of cases. The most common associated lesions are arch abnormalities including interrupted aortic arch and coarctation of the aorta. Other less common associated lesions may also occur. Antenatal diagnosis is rare. In the current era, early mortality following repair of simple aortopulmonary window approaches zero percent and depends on the presence of associated lesions especially interrupted aortic arch. Long-term outcome should be excellent. Early morbidity includes pulmonary artery stenosis and residual aortopulmonary septal defects. Long-term follow-up is indicated to look for recurrent lesions such as the development of branch pulmonary artery stenosis and arch obstruction.

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Author information

Authors and Affiliations

  1. Department of Cardiothoracic Surgery, The Heart Institute, Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, USA

    Awais Ashfaq, Michael Barnes & James S. Tweddell

  2. Division of Cardiothoracic Surgery, Department of Surgery, Medical College of Wisconsin, Wauwatosa, WI, USA

    Moritz C. Wyler von Ballmoos

  3. Department of Pediatrics, Division of Pediatric Cardiology, The Herma Heart Center The Medical College of Wisconsin, Children’s Hospital of Wisconsin, Milwaukee, WI, USA

    Stuart Berger

  4. Department of Cardiothoracic Surgery, Children’s Hospital of Wisconsin, Milwaukee, WI, USA

    Michael E. Mitchell

Authors
  1. Awais Ashfaq
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  2. Moritz C. Wyler von Ballmoos
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  3. Michael Barnes
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  4. Stuart Berger
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  5. Michael E. Mitchell
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  6. James S. Tweddell
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Corresponding author

Correspondence to Awais Ashfaq .

Editor information

Editors and Affiliations

  1. Children’s Hospital Colorado University of Colorado Denver, School of, Aurora, CO, USA

    Eduardo M. da Cruz

  2. Children's Hospital Colorado University of Colorado School of Medicin, Aurora, CO, USA

    Dunbar Ivy

  3. Department of Cardiac Surgery, German Pediatric Heart Center, Sankt Augustin, Germany

    Viktor Hraska

  4. Pediatric Cardiac Surgery, Children's Hospital Colorado University of Colorado, Aurora, CO, USA

    James Jaggers

Section Editor information

  1. The Heart Institute, Department of Pediatrics, Children’s Hospital Colorado, University of Colorado School of Medicine, Aurora, CO, USA

    Eduardo M. da Cruz

  2. The Heart Institute, Pediatric Cardiac Surgery, Children’s Hospital Colorado, University of Colorado School of Medicine, Aurora, CO, USA

    James Jaggers

  3. Cardiothoracic Surgery, University of Colorado School of Medicine The Children’s Hospital Pediatrics, Aurora, CO, USA

    James Jaggers

  4. Dept. Pediatric Cardiology, Children's Hospital Colorado, Univ. of Colorado, Denver, Aurora, Colorado, USA

    Dunbar Ivy

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Ashfaq, A., Wyler von Ballmoos, M.C., Barnes, M., Berger, S., Mitchell, M.E., Tweddell, J.S. (2020). Aortopulmonary Window. In: da Cruz, E.M., Ivy, D., Hraska, V., Jaggers, J. (eds) Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care. Springer, London. https://doi.org/10.1007/978-1-4471-4999-6_17-2

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  • DOI: https://doi.org/10.1007/978-1-4471-4999-6_17-2

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-4999-6

  • Online ISBN: 978-1-4471-4999-6

  • eBook Packages: Springer Reference MedicineReference Module Medicine

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