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Pediatric Surgery pp 1213-1235 | Cite as

Spina Bifida and Encephalocele

  • Jonathan R. EllenbogenEmail author
  • Michael D. Jenkinson
  • Conor L. Mallucci
Reference work entry

Abstract

This chapter aims to explain the range of congenital anomies that are encompassed by the term neural tube defects (NTD). Both cranial and spinal abnormalities occur which arise during embryological development due to defects in morphogenesis of the neural tube. They range from anencephaly to spina bifida occulta. The commonest congenital nervous system defect encountered remains spina bifida despite the overall incidence of neural tube defects declining. The chapter explains the classification, pathogenesis, assessment, management, treatment, and prognosis related to these conditions.

Keywords

Hydrocephalus Cerebrospinal fluid (CSF) Ultrasound Computed tomography (CT) Magnetic resonance imaging (MRI) Shunt Neural tube defects (NTD) Spina bifida Anencephaly Myelomeningocele Embryology Encephalocele Meningocele Serum alphafetoprotein Counseling In-utero surgery Hydrocephalus Arnold–Chiari type II malformation Craniorachischisis Dysraphism 

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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2020

Authors and Affiliations

  • Jonathan R. Ellenbogen
    • 1
    • 2
    Email author
  • Michael D. Jenkinson
    • 2
  • Conor L. Mallucci
    • 1
  1. 1.Department of NeurosurgeryAlder Hey Children’s NHS Foundation TrustLiverpoolUK
  2. 2.Department of NeurosurgeryThe Walton Centre NHS Foundation TrustLiverpoolUK

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