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Klüver-Bucy Syndrome

  • Reference work entry
  • First Online:
Encyclopedia of Clinical Neuropsychology

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Synonyms

KBS; Temporal lobe syndrome

Short Description or Definition

Klüver-Bucy syndrome (KBS) is a disorder classically associated with bilateral extirpation of the temporal lobe, including most of the hippocampus and amygdala, resulting in six core symptoms: (1) visual agnosia, (2) hyperorality, (3) hypermetamorphosis, (4) alterations in emotional behavior, (5) changes in sexual behavior, and (6) changes in dietary habits. The initial work of Klüver and Bucy (1937, 1938, 1939) was important in furthering understanding of the function of the temporal lobes and associated structures, Papez’s neuroanatomic circuit of emotion (Papez 1937), as well as neurobehavioral phenomena including amnesia and agnosia. Though comparatively scarce, case descriptions of KBS are uniformly rich.

Categorization

Both partial and complete KBS involving animals and humans have been reported. Human KBS syndrome has been described in children, adolescents, and adults. Following the suggestion of Lilly,...

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Author information

Authors and Affiliations

  1. Intermountain Healthcare and University of Utah Center on Aging, Salt Lake City, UT, USA

    Kelly Davis Garrett

  2. Psychology Department, West Chester University of Pennsylvania, West Chester, PA, USA

    Farzin Irani

  3. Departments of Geriatrics, Gerontology, and Psychology, Rowan University, New Jersey Institute for Successful Aging, School of Osteopathic Medicine, Stratford, NJ, USA

    David J. Libon

  4. Department of Psychiatry and Behavioral Science, University of North Dakota School of Medicine, Fargo, ND, USA

    Rod Swenson

Authors
  1. Kelly Davis Garrett
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  2. Farzin Irani
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  3. David J. Libon
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  4. Rod Swenson
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Corresponding author

Correspondence to Farzin Irani .

Editor information

Editors and Affiliations

  1. Department of Physical Medicine and Rehabilitation, Virginia Commonwealth University, Richmond, VA, USA

    Jeffrey S. Kreutzer

  2. Kessler Foundation, Pleasant Valley Way, West Orange, NJ, USA

    John DeLuca

  3. Independent Practice, Wynnewood, PA, USA

    Bruce Caplan

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Garrett, K.D., Irani, F., Libon, D.J., Swenson, R. (2018). Klüver-Bucy Syndrome. In: Kreutzer, J.S., DeLuca, J., Caplan, B. (eds) Encyclopedia of Clinical Neuropsychology. Springer, Cham. https://doi.org/10.1007/978-3-319-57111-9_1618

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