Limited Dorsal Spinal Nondisjunctional Disorders: Limited Dorsal Myeloschisis, Congenital Spinal Dermal Sinus Tract, and Mixed Lesions

  • Sui-To WongEmail author
  • Amanda Kan
  • Dachling PangEmail author
Living reference work entry


Spinal dysraphic lesions due to incomplete fusion and consequent failed disjunction of a limited segment of the dorsal neural tube during primary neurulation are the subjects of this chapter. We use the term “limited dorsal spinal nondisjunctional disorders” (LDSNDs) to encompass several known varieties of such lesions, namely, limited dorsal myeloschisis (LDM), congenital spinal dermal sinus tract (CSDST), mixed lesions of the two, and other closely related complex lesions (Wang et al. 1993; Pang et al. 2013a; Eibach et al. 2017). All of these probably share a common embryogenetic mechanism and similar clinical manifestations.


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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Department of NeurosurgeryTuen Mun HospitalHong KongChina
  2. 2.Department of Clinical PathologyTuen Mun HospitalHong KongChina
  3. 3.University of CaliforniaDavisUSA
  4. 4.Great Ormond Street Hospital For Children, NHS TrustLondonUK

Section editors and affiliations

  • Dachling Pang
    • 1
  • Kyu-Chang Wang
    • 2
    • 3
  • Dominic N. P. Thompson
    • 4
  1. 1.LondonUK
  2. 2.Division of Pediatric NeurosurgerySeoul National University Children’s HospitalSeoulSouth Korea
  3. 3.Division of Pediatric NeurosurgerySeoul National University Children’s Hospital & Seoul National University College of MedicineSeoulSouth Korea
  4. 4.Department of NeurosurgeryGreat Ormond Street HospitalLondonUK

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