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Benign soft tissue tumor composed of benign-appearing spindle cells set in an abundant myxoid hypovascular stroma.
It is a rare tumor. It may occur sporadically or in the context of Mazabraud syndrome (single or multiple intramuscular myxomas associated with monostotic or polyostotic fibrous dysplasia) (Nielsen and Hogendoorn 2013).
It generally affects adult patients, with a peak in the fourth to seventh decades of life.
Females are more frequently affected than males.
It generally arises in the extremities, especially in the thigh.
Simple surgical excision is curative.
It is a benign lesion, with a low risk of local recurrence after incomplete surgery. No malignant transformation has been reported (Nielsen and Hogendoorn 2013).
- Nielsen, G. P., & Hogendoorn, P. C. W. (2013). Intramuscular myxoma. In C. D. M. Fletcher, J. A. Bridge, P. C. W. Hogendoorn, & F. Mertens (Eds.), World Health Organization classification of tumours. Pathology and genetics of tumours of soft tissue and bone (pp. 195–196). Lyon: IARC Press.Google Scholar