Synonyms
Frontotemporal lobar degeneration; Logopenic aphasia; Pick’s disease; Progressive fluent aphasia; Progressive nonfluent aphasia; Semantic dementia
Glossary
- AD:
-
Alzheimer’s disease
- ADD/ADHD:
-
Attention deficit disorder/Attention deficit hyperactivity disorder
- ALS:
-
Amyotrophic lateral sclerosis (Lou Gehrig’s disease)
- AOS:
-
Apraxia of speech
- ApoE4:
-
Apolipoprotein E4
- bvFTD:
-
Behavioral variant frontotemporal dementia
- C90rf72:
-
Chromosome 9 open reading frame 72; in normal individuals, there are 2–24 noncoding hexanucleotide GGGGCC repeats. Expansion to hundreds to thousands of repeats occurs in individuals with frontotemporal dementia and amyotrophic lateral sclerosis. The smallest expansion conferring risk is not known. It is the most common gene causing either frontotemporal dementia or amyotrophic lateral sclerosis. The second most common presentation of mutations in this gene after behavioral variant primary progressive aphasia is nonfluent variant primary progressive aphasia
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Shatz, R. (2018). Primary Progressive Aphasia. In: Kreutzer, J.S., DeLuca, J., Caplan, B. (eds) Encyclopedia of Clinical Neuropsychology. Springer, Cham. https://doi.org/10.1007/978-3-319-57111-9_915
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