Synonyms
Neuroendocrine carcinoma; Neuroendocrine tumors; Small cell carcinoma
Definition
Neuroendocrine neoplasms very rarely occur in the anus. There is no case of anal carcinoid tumor described in the literature, but some cases have perhaps been assimilated to rectal tumors. There are only rare isolated case reports of anal neuroendocrine carcinoma, small cell neuroendocrine carcinoma, and composite neuroendocrine carcinoma – in situ squamous cell carcinoma or adenocarcinoma published in the literature.
Clinical Features
Patients complain of anal pain, rectal bleeding, and the presence of a perianal mass.
Site
The neuroendocrine tumors probably arise from neuroendocrine cells residing in colorectal type mucosa or in the anal transitional zone mucosa.
Incidence, age, sex
Due to the rarity of these tumors, it is difficult to assess the prevalence of this entity, the sex ratio, and the age of patients.
Treatment
There is no standard treatment for this rare tumor. A few patients have...
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
References and Further Reading
Eberhardt, J. M., Brown, K., Lo, S., Nagda, S., & Yong, S. (2012). Extrapulmonary small cell carcinoma of the anal canal: A case report and review of the literature. Case Reports in Medicine, 2012, 341432.
Shia, J. (2010). An update on tumors of the anal canal. Archives of Pathology & Laboratory Medicine, 134, 1601–1611.
Author information
Authors and Affiliations
Editor information
Editors and Affiliations
Rights and permissions
Copyright information
© 2017 Springer International Publishing AG
About this entry
Cite this entry
Chatelain, D., Fléjou, JF. (2017). Neuroendocrine Neoplasms of the Anus. In: Carneiro, F., Chaves, P., Ensari, A. (eds) Pathology of the Gastrointestinal Tract. Encyclopedia of Pathology. Springer, Cham. https://doi.org/10.1007/978-3-319-40560-5_2865
Download citation
DOI: https://doi.org/10.1007/978-3-319-40560-5_2865
Published:
Publisher Name: Springer, Cham
Print ISBN: 978-3-319-40559-9
Online ISBN: 978-3-319-40560-5
eBook Packages: MedicineReference Module Medicine