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Lymphoma and Immunoproliferative Small Intestinal Disease (IPSID)

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  • First Online:
Pathology of the Gastrointestinal Tract

Part of the book series: Encyclopedia of Pathology ((EP))

  • 274 Accesses

Synonyms

Intestinal lymphoma: “Western-type” intestinal lymphoma

Immunoproliferative small intestinal disease (IPSID): Alpha chain disease; Mediterranean lymphoma; Seligmann disease

Monomorphic epitheliotropic intestinal T-cell lymphoma: Defined as “Enteropathy-associated T-cell lymphoma type” in World Health Organization (WHO) classification of tumors of haematopoietic and lymphoid tissues in 2008 and as “Monomorphic CD56 (+) intestinal T-cell lymphoma” in WHO Classification of Tumours of the Digestive System in 2010. The 2016 revision of the classification of lymphoid neoplasms defines the entity as “Monomorphic epitheliotropic intestinal T-cell lymphoma.”

Definition

Intestinal Lymphoma (IL)

The definition of “intestinal lymphoma (IL)” varies among the authors as it can occur as a primary lesion or in a secondary fashion in a substantial portion of the cases. Usually a “primary” gastrointestinal (GI) lymphoma is considered when the main bulk of disease is located in GI tract with...

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Abbreviations

BL:

Burkitt lymphoma

DLBCL:

Diffuse large B-cell lymphoma

DLBCL/BL, unclassifiable:

Lymphoma, unclassifiable, with features intermediate between DLBCL and BL

EATL/EATL-I:

Enteropathy-associated T-cell lymphoma-type-I

EATL-II:

Enteropathy-associated T-cell lymphoma, type II (synonym with “Monomorphic epitheliotropic intestinal T-cell lymphoma”)

EBV+ DLBCL of elderly:

EBV-positive diffuse large B-cell lymphoma of elderly

ENKTL:

Extranodal NK/T-cell lymphoma

FL:

Follicular lymphoma

IPSID:

Immunoproliferative small intestinal disease

MALT lymphoma:

Mucosa-associated lymphoid tissue lymphoma

MCL:

Mantle cell lymphoma

MEITL:

Monomorphic epitheliotropic intestinal T-cell lymphoma

NHL:

Non-Hodgkin lymphoma

PBL:

Plasmablastic lymphoma

References and Further Reading

  • Al-Saleem, T., & Al-Mondhiry, H. (2005). Immunoproliferative small intestinal disease (IPSID): A model for mature B-cell neoplasms. Blood, 105, 2274–2280.

    Article  CAS  Google Scholar 

  • Arora, N., Manipadam, M. T., Pulimood, A., Ramakrishna, B. S., Chacko, A., Kurian, S. S., & Nair, S. (2011). Gastrointestinal lymphomas: Pattern of distribution and histological subtypes: 10 years experience in a tertiary centre in South India. Indian Journal of Pathology and Microbiology, 54, 712–719.

    Article  Google Scholar 

  • Bautista-Quach, M. A., Ake, C. D., Chen, M., & Wang, J. (2012). Gastrointestinal lymphomas: Morphology, immunophenotype and molecular features. Journal of Gastrointestinal Oncology, 3, 209–225.

    PubMed  PubMed Central  Google Scholar 

  • Bosman, F., Carneiro, F., Hruban, R. H., & Theise, N. D. (Eds.). (2010). WHO classification of tumours of the digestive system. Lyon: IARC.

    Google Scholar 

  • Swerdlow, S. H., Campo, E., Harris, N. L., Jaffe, E. S., Pileri, S. A., Stein, H., Thiele, J., & Vardiman, J. W. (Eds.). (2008). WHO classification of tumours of haematopoietic and lymphoid tissues (4th ed.). Lyon: IARC.

    Google Scholar 

  • Swerdlow, S. H., Campo, E., Pileri, S. A., Harris, N. L., Stein, H., Siebert, R., Advani, R., Ghielmini, M., Salles, G. A., Zelenetz, A. D., & Jaffe, E. S. (2016). The 2016 revision of the World Health Organization (WHO) classification of lymphoid neoplasms. Blood, 127, 2391–2405. pii: blood-2016-01-643569. [Epub ahead of print].

    Article  Google Scholar 

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Author information

Authors and Affiliations

  1. Department of Pathology, Ege University Medical School, Bornova, Izmir, Turkey

    Başak Doğanavşargil

Authors
  1. Başak Doğanavşargil
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Corresponding author

Correspondence to Başak Doğanavşargil .

Editor information

Editors and Affiliations

  1. Faculty of Medicine of Porto University, Centro Hospitalar São João and Ipatimup/i3S, Porto, Portugal

    Fátima Carneiro

  2. Serviço de Anatomia Patológica, Instituto Português de Oncologia de Lisboa de Francisco Gentil, Lisbon, Portugal

    Paula Chaves

  3. Faculdade de Ciências da Saúde, Universidade da Beira Interior, Covilhã, Portugal

    Paula Chaves

  4. Department of Pathology, Ankara University Medical School, Sihhiye, Ankara, Turkey

    Arzu Ensari

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Doğanavşargil, B. (2017). Lymphoma and Immunoproliferative Small Intestinal Disease (IPSID). In: Carneiro, F., Chaves, P., Ensari, A. (eds) Pathology of the Gastrointestinal Tract. Encyclopedia of Pathology. Springer, Cham. https://doi.org/10.1007/978-3-319-40560-5_1505

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  • DOI: https://doi.org/10.1007/978-3-319-40560-5_1505

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-40559-9

  • Online ISBN: 978-3-319-40560-5

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