1. Preface

   • S. W. Moses
   • Y. S. Shin
   • K. Ullrich

   EditorialNotes Pages: 1 - 1

2. Introduction

   • S. W. Moses

   EditorialNotes Pages: 1 - 1

3. Human microsomal glucose-6-phosphatase system

   • R. C. Nordlie
   • K. A. Sukalski
   • W. T. Johnson

   Biochemistry of Glucose-6-Phosphatase system and diagnosis Pages: 2 - 6

4. Glucose-6-phosphatase and type 1 glycogen storage disease: Some critical considerations

   • W. J. Arion
   • W. K. Canfield

   Biochemistry of Glucose-6-Phosphatase system and diagnosis Pages: 7 - 13

5. Identification, purification and genetic deficiencies of the glucose-6-phosphatase system transport proteins

   • I. D. Waddell
   • A. Burchell

   Biochemistry of Glucose-6-Phosphatase system and diagnosis Pages: 14 - 17

6. The molecular basis of the genetic deficiencies of five of the components of the glucose-6-phosphatase system: Improved diagnosis

   • A. Burchell
   • I. D. Waddell

   Biochemistry of Glucose-6-Phosphatase system and diagnosis Pages: 18 - 21

7. Purification of human microsomal liver glucose-6-phosphatase system by affinity chromatography and immunodetection

   • S. Kösel
   • D. Matern
   • Y. S. Shin

   Biochemistry of Glucose-6-Phosphatase system and diagnosis Pages: 22 - 25

8. Cytosolic free Ca²⁺ signals in single adherent human neutrophils: Generation and functional role

   • M. E. E. Jaconi
   • J. M. Theler
   • P. D. Lew

   Neutrophiles and GSD type Ib Pages: 26 - 32

9. Defective neutrophil and monocyte functions in glycogen storage disease type Ib: A literature review

   • R. Gitzelmann
   • N. U. Bosshard

   Neutrophiles and GSD type Ib Pages: 33 - 38

10. Impairment of calcium mobilization in phagocytic cells in glycogen storage disease type 1b

    • H. M. Korchak
    • B. -Z. Garty
    • L. Kilpatrick

    Neutrophiles and GSD type Ib Pages: 39 - 43

11. Deficient glucose phosphorylation as a possible common denominator and its relation to abnormal leucocyte function, in glycogen storage disease 1b patients

    • N. Bashan
    • R. Potashnik
    • S. W. Moses

    Neutrophiles and GSD type Ib Pages: 44 - 48

12. Glycogen storage disease type Ib: Infectious complications and measures for prevention

    • U. Wendel
    • H. Schroten
    • V. Wahn

    Neutrophiles and GSD type Ib Pages: 49 - 51

13. The long-term outcome of patients with glycogen storage disease type Ia

    • G. P. A. Smit

    Treatment and complications in GSD type Ib Pages: 52 - 55

14. Type I glycogen storage disease: Nine years of management with cornstarch

    • Y. -T. Chen
    • C. H. Bazzarre
    • R. A. Coleman

    Treatment and complications in GSD type Ib Pages: 56 - 59

15. Renal complications in glycogen storage disease type I

    • W. C. C. Reitsma-Bierens

    Treatment and complications in GSD type Ib Pages: 60 - 62

16. Glycogen storage disease I and hepatocellular tumours

    • L. Bianchi

    Treatment and complications in GSD type Ib Pages: 63 - 70

17. Liver transplantation for type I and type IV glycogen storage disease

    • R. Selby
    • T. E. Starzl
    • R. S. Kendall

    Treatment and complications in GSD type Ib Pages: 71 - 76

18. Glucose-6-phosphate: A key compound in glycogenosis I and favism leading to hyper- or hypolipidaemia

    • G. Schmitz
    • H. Hohage
    • K. Ullrich

    Treatment and complications in GSD type Ib Pages: 77 - 84

19. Biochemical aspects of glycogen storage disease type I: Summary of the discussions

    • Y. Shin

    Summary of the discussions Pages: 85 - 86

20. Clinical aspects of glycogen storage disease type I: Summary of the discussions

    • K. Ullrich
    • G. P. A. Smit

    Summary of the discussions Pages: 87 - 88