Atypical Autosomal Recessive AID Deficiency—Yet Another Piece of the Hyper-IgM Puzzle Erika Della MinaStuart G. Tangye Commentary 25 March 2022 Pages: 713 - 715
Elevated CD21low B Cell Frequency Is a Marker of Poor Immunity to Pfizer-BioNTech BNT162b2 mRNA Vaccine Against SARS-CoV-2 in Patients with Common Variable Immunodeficiency Peter BergmanDavid WullimannC. I. Edvard Smith Original Article Open access 15 March 2022 Pages: 716 - 727
COVID-19 Vaccine Uptake and Efficacy in a National Immunodeficiency Cohort Mark J. PonsfordKimberly EvansOn behalf of the Immunodeficiency Centre for Wales and Division of Population Medicine Letter to Editor 11 February 2022 Pages: 728 - 731
Post-SARS-CoV-2 Vaccine Monitoring of Disease Flares in Autoinflammatory Diseases Sara AlehashemiEvelien van GelderenRaphaela Goldbach-Mansky Letter to Editor 15 February 2022 Pages: 732 - 735
First Identified Case of Fatal Fulminant Eosinophilic Myocarditis Following the Initial Dose of the Pfizer-BioNTech mRNA COVID-19 Vaccine (BNT162b2, Comirnaty): an Extremely Rare Idiosyncratic Necrotizing Hypersensitivity Reaction Different to Hypersensitivity or Drug-Induced Myocarditis Nicholas G. KounisIoanna KoniariGrigorios Tsigkas Letter to Editor 17 February 2022 Pages: 736 - 737
Low Lymphocytes and IFN-Neutralizing Autoantibodies as Biomarkers of COVID-19 Mortality Jesús TroyaPaul BastardAurora Pujol Letter to Editor 03 March 2022 Pages: 738 - 741
Transient Increase of Pre-existing Anti-IFN-α2 Antibodies Induced by SARS-CoV-2 Infection Sophie SteelsJan Van ElslandeXavier Bossuyt Letter to Editor 17 March 2022 Pages: 742 - 745
22q11.2 Deletion and Duplication Syndromes and COVID-19 T. Blaine CrowleyDonna McDonald McGinnInternational q11.2 COVID group report Letter to Editor 18 March 2022 Pages: 746 - 748
Diagnosis of APS-1 in Two Siblings Following Life-Threatening COVID-19 Pneumonia Laire SchidlowskiAna Paula Diniz IwamuraCarolina Prando Letter to Editor 19 March 2022 Pages: 749 - 752
Lymphocytes Utilize Somatic Mutations, Epigenetic Silencing, and the Proteasome to Escape Truncated WASP Expression Caroline KhannaCarole Le CozNeil Romberg Original Article 12 February 2022 Pages: 753 - 759
Pneumococcal IgG Antibody Responses to 23vPPV in Healthy Controls Using an Automated ELISA Laine M. HoskingKirsten P. PerrettSharon Choo Original Article 01 March 2022 Pages: 760 - 770
A Novel AICDA Splice-Site Mutation in Two Siblings with HIGM2 Permits Somatic Hypermutation but Abrogates Mutational Targeting Johannes DirksGabriele HaaseHenner Morbach Original Article Open access 05 March 2022 Pages: 771 - 782
Progressive Depletion of B and T Lymphocytes in Patients with Ataxia Telangiectasia: Results of the Italian Primary Immunodeficiency Network Emilia CirilloAgata PolizziClaudio Pignata Original Article Open access 08 March 2022 Pages: 783 - 797
Loss of Function Mutation in ELF4 Causes Autoinflammatory and Immunodeficiency Disease in Human Gan SunLuyao QiuHongqiang Du Original Article 09 March 2022 Pages: 798 - 810
Health-Related Quality of Life in 91 Patients with X-Linked Agammaglobulinemia Katherine AltmanChuan ZhouM. Teresa de la Morena Original Article 14 March 2022 Pages: 811 - 818
Hematopoietic Cell Transplantation for Adenosine Deaminase Severe Combined Immunodeficiency—Improved Outcomes in the Modern Era Elisabetta GhimentonAisling FlinnAndrew R. Gennery Original Article Open access 15 March 2022 Pages: 819 - 826
X-Linked Agammaglobulinemia: Infection Frequency and Infection-Related Mortality in the USIDNET Registry Dana O’TooleDaniel GrothElizabeth Feuille Original Article 15 March 2022 Pages: 827 - 836
Activated Phosphoinositide 3-Kinase δ Syndrome: a Large Pediatric Cohort from a Single Center in China Luyao QiuYanping WangXiaodong Zhao Original Article 16 March 2022 Pages: 837 - 850
TCRαβ-Depleted Haploidentical Grafts Are a Safe Alternative to HLA-Matched Unrelated Donor Stem Cell Transplants for Infants with Severe Combined Immunodeficiency Christo TsilifisSu Han LumAndrew R. Gennery Original Article Open access 19 March 2022 Pages: 851 - 858
Fatal and Unresponsive Cytomegalovirus Infection in a New Homozygous FOXN1 Gene Variation Causing Nude SCID Herberto Jose Chong-NetoGesmar Rodrigues Silva SegundoIEI-CHC Team Letter to Editor 22 January 2022 Pages: 859 - 861
Correction to: Fatal and Unresponsive Cytomegalovirus Infection in a New Homozygous FOXN1 Gene Variation Causing Nude SCID Herberto Jose Chong‑NetoGesmar Rodrigues Silva SegundoIEI-CHC Team Correction 21 March 2022 Pages: 862 - 862
A Case Report of Fatal Mucormycosis in a 30-Year-Old Patient with Autoimmune Polyendocrine Syndrome Type 1 Jacob M. RosenbergJulian A. VillalbaMichail S. Lionakis Letter to Editor 10 February 2022 Pages: 863 - 865
STAT 3 GOF with Polycythemia: a Twist to the Tale-First Case Report from India Vijaya GowriPrasad TaurMukesh Desai Letter to Editor 15 February 2022 Pages: 866 - 868
Fatal JC-virus Granular Cerebellar Neuronopathy in a Patient Diagnosed with ALPS and Hypogammaglobulinemia Jannik Helweg-LarsenMorten RasmussenAnders Fomsgaard Letter to Editor 17 February 2022 Pages: 869 - 872
Peeling Skin Syndrome Type 1: Dupilumab Reduces IgE, But Not Skin Anomalies Barranca AlexisJonca NathalieMazereeuw-Hautier Juliette Letter to Editor 23 February 2022 Pages: 873 - 875
Inborn Errors of Immunity in Latvia: Analysis of Data from 1994 to 2020 Tatjana ProkofjevaZane LucaneNatalja Kurjane Letter to Editor Open access 24 February 2022 Pages: 876 - 879
Early Onset of TNFα-Driven Arthritis, Auto-inflammation, and Progressive Loss of Vision in a Patient with ALPK1 Mutation Julia HeckerMarilena LetiziaCarl Weidinger Letter to Editor Open access 02 March 2022 Pages: 880 - 884
A Novel Kindred with MyD88 Deficiency Giorgia BucciolLeen MoensIsabelle Meyts Letter to Editor 14 March 2022 Pages: 885 - 888
Recurrent Breast Abscesses in a Female with Autosomal Dominant Hyper-IgE Syndrome Vibha SzafronSohail R. ShahNicholas L. Rider Letter to Editor 15 March 2022 Pages: 889 - 891
PEPD-Related Prolidase Deficiency Presenting as Hyper-immunoglobulin E Syndrome Ritasman BaisyaPrajnya RanganathLiza Rajasekhar Letter to Editor 16 March 2022 Pages: 892 - 897
Lung MRI- Changing Paradigms in Evaluation of Chronic Granulomatous Disease in Children Kushaljit Singh SodhiRicha GaubaJoseph L Mathew Letter to Editor 16 March 2022 Pages: 898 - 900
A Case of XIAP Deficiency Successfully Managed with Tadekinig Alfa (rhIL-18BP) Ashley V. GeerlinksAndrea M. DvorakXIAP Deficiency Treatment Consortium Letter to Editor 19 March 2022 Pages: 901 - 903
Prevalence of APECED-Like Clinical Disease in an Electronic Health Record Database, USA Emily E. RicottaElise M. N. FerréMichail S. Lionakis Letter to Editor 21 March 2022 Pages: 904 - 906
Oral Ulcers Resolution Using IL12/23 Blockade in an Infant with Leukocyte Adhesion Deficiency Type 1 Benjamin FournierBénédicte NevenMartin Biosse Duplan Letter to Editor 21 March 2022 Pages: 907 - 909
Correction to: Hemophagocytic lymphohistiocytosis in activated PI3K delta syndrome, an illustrative case report Zijun ZhouTimo ZondagJan A. M. Laar Correction 09 February 2022 Pages: 910 - 910
