In memoriam: Stephen J Seligman, MD Jean-Laurent CasanovaQian ZhangEmmanuelle Jouanguy Commentary Open access 14 January 2022 Pages: 437 - 440
First Identified Case of Fatal Fulminant Necrotizing Eosinophilic Myocarditis Following the Initial Dose of the Pfizer-BioNTech mRNA COVID-19 Vaccine (BNT162b2, Comirnaty): an Extremely Rare Idiosyncratic Hypersensitivity Reaction Rohan AmeratungaSee-Tarn WoonRexson D. Tse Original Article 03 January 2022 Pages: 441 - 447
Seasonal Betacoronavirus Antibodies’ Expansion Post-BNT161b2 Vaccination Associates with Reduced SARS-CoV-2 VoC Neutralization Stefania DispinseriIlaria MarzinottoVito Lampasona Original Article Open access 09 January 2022 Pages: 448 - 458
Autoantibodies Neutralizing Type I Interferons in 20% of COVID-19 Deaths in a French Hospital Angélique Chauvineau-GrenierPaul BastardBenjamin Rossi Original Article 27 January 2022 Pages: 459 - 470
Inherited IFNAR1 Deficiency in a Child with Both Critical COVID-19 Pneumonia and Multisystem Inflammatory Syndrome Hassan AbolhassaniNils LandegrenQiang Pan-Hammarström Original Article Open access 28 January 2022 Pages: 471 - 483
The Immune Deficiency and Dysregulation Activity (IDDA2.1 ‘Kaleidoscope’) Score and Other Clinical Measures in Inborn Errors of Immunity Markus G. SeidelVictoria K. TeschMartin Benesch Original Article Open access 19 November 2021 Pages: 484 - 498
Correction to: The Immune Deficiency and Dysregulation Activity (IDDA2.1 ‘Kaleidoscope’) Score and Other Clinical Measures in Inborn Errors of Immunity Markus G. SeidelVictoria K. TeschMartin Benesch Correction Open access 09 February 2022 Pages: 499 - 499
A Multi‑Center, Open‑Label, Single‑Arm Trial to Evaluate the Efficacy, Pharmacokinetics, and Safety and Tolerability of IGSC 20% in Subjects with Primary Immunodeficiency Manuel SantamariaOlaf NethJiang Lin Original Article Open access 01 January 2022 Pages: 500 - 511
Correction to: A Multi-center, Open-Label, Single-Arm Trial to Evaluate the Efficacy, Pharmacokinetics, and Safety and Tolerability of IGSC 20% in Subjects with Primary Immunodeficiency Manuel SantamariaOlaf NethJiang Lin Correction Open access 16 February 2022 Pages: 512 - 513
CD40 Ligand Deficiency in Latin America: Clinical, Immunological, and Genetic Characteristics Tábata Takahashi FrançaLucila Akune BarreirosAntonio Condino-Neto Original Article 04 January 2022 Pages: 514 - 526
Correction to: CD40 Ligand Deficiency in Latin America: Clinical, Immunological, and Genetic Characteristics Tábata Takahashi FrançaLucila Akune BarreirosAntonio Condino‑Neto Correction 07 February 2022 Pages: 527 - 528
Hematopoietic Cell Transplantation for Inborn Errors of Immunity Other than Severe Combined Immunodeficiency in Japan: Retrospective Analysis for 1985–2016 Satoshi MiyamotoKatsutsugu UmedaTomohiro Morio Original Article 04 January 2022 Pages: 529 - 545
Antiviral T-Cell Frequencies in a Healthy Population: Reference Values for Evaluating Antiviral Immune Cell Profiles in Immunocompromised Patients Friederike C. Schulze LammersAgnes BonifaciusBritta Eiz-Vesper Original Article Open access 06 January 2022 Pages: 546 - 558
Identification of Germline Non-coding Deletions in XIAP Gene Causing XIAP Deficiency Reveals a Key Promoter Sequence Zineb SbihiKay TanitaSylvain Latour Original Article 09 January 2022 Pages: 559 - 571
Predictive Factors for and Complications of Bronchiectasis in Common Variable Immunodeficiency Disorders Johannes M. SperlichBodo GrimbacherJohn R. Hurst Original Article Open access 11 January 2022 Pages: 572 - 581
Low Density Granulocytes and Dysregulated Neutrophils Driving Autoinflammatory Manifestations in NEMO Deficiency Naz Surucu YilmazSevgi Bilgic EltanMayda Gursel Original Article 14 January 2022 Pages: 582 - 596
Cocktails of KLK5 Protease Inhibitors and Anti-TNFα Therapeutics: an Effective Treatment for Netherton Syndrome Eleni ZingkouGeorgios PampalakisGeorgia Sotiropoulou Original Article 18 January 2022 Pages: 597 - 605
Life-Threatening Enterovirus 71 Encephalitis in Unrelated Children with Autosomal Dominant TLR3 Deficiency Chen-Yen KuoCheng-Lung KuTzou-Yien Lin Original Article 18 January 2022 Pages: 606 - 617
Long-Term Follow-Up of Newborns with 22q11 Deletion Syndrome and Low TRECs Jenny Lingman FrammeChristina LundqvistOlov Ekwall Original Article Open access 26 January 2022 Pages: 618 - 633
Expanding the Clinical and Immunological Phenotypes and Natural History of MALT1 Deficiency Asena Pinar SeferHassan AbolhassaniSafa Baris Original Article 26 January 2022 Pages: 634 - 652
Comprehensive Assessment of Skin Disorders in Patients with Common Variable Immunodeficiency (CVID) Ali Zarezadeh MehrabadiNazanin AghamohamadiReza Yazdani Original Article 27 January 2022 Pages: 653 - 664
Clinical Outcome and Underlying Genetic Cause of Functional Terminal Complement Pathway Deficiencies in a Multicenter UK Cohort Annalie ShearsCathal SteelePeter D. Arkwright Original Article Open access 27 January 2022 Pages: 665 - 671
Clinicopathological Manifestations and Immune Phenotypes in Adult-Onset Immunodeficiency with Anti-interferon-γ Autoantibodies Yi-Chun ChenShao-Wen WengWan-Ting Huang Original Article 28 January 2022 Pages: 672 - 683
To the Editor: “Complete Resolution of Multiple Warts after a First Dose of the Receptor Interleukin-5 Inhibitor” Kissy Guevara-HoyerEduardo de la Fuente-MunozSilvia Sánchez-Ramón Letter to Editor 04 January 2022 Pages: 684 - 687
Activated PI3 Kinase Delta Syndrome Revealed by Vasculitis and Disseminated Toxoplasmosis Aurore LarrauffieCharlotte SyrykhJeremie Dion Letter to Editor 13 January 2022 Pages: 688 - 690
A De Novo Cause of PGM3 Deficiency Treated with Hematopoietic Stem Cell Transplantation Andrew WinslowElizabeth R. JalazoTimothy Moran Letter to Editor 18 January 2022 Pages: 691 - 694
Psychological Symptoms in Primary Immunodeficiencies: a Common Comorbidity? Olivia R. ManusamaNico J. M. van BeverenVirgil A. S. H. Dalm Letter to Editor Open access 19 January 2022 Pages: 695 - 698
Malignancy in STAT3 Deficient Hyper IgE Syndrome Amanda UrbanNCI Lymphoma Physicians ConsortiumAlexandra F. Freeman Letter to Editor 21 January 2022 Pages: 699 - 702
Hematopoietic Cell Transplant for CD40 Ligand Deficiency—Comparing Busulfan Versus Treosulfan Vicky-Anne CarruthersSu Han LumAndrew R. Gennery Letter to Editor 28 January 2022 Pages: 703 - 705
Vanishing Lymphocytes in a Case of Vanishing Bone Disease Vaishnavi V. IyengarVijaya GowriMukesh M. Desai Letter to Editor 28 January 2022 Pages: 706 - 708
A Pitfall of Whole Exome Sequencing: Variants in the 5′UTR Splice Site of BTK Causing XLA Sanami TakadaIngrid Pico-KnijnenburgMirjam van der Burg Letter to Editor 29 January 2022 Pages: 709 - 712