A Novel Recessive Mutation of Interferon-γ Receptor 1 in a Patient with Mycobacterium tuberculosis in Bone Marrow Aspirate Mahsima ShabaniSoheila AleyasinNima Rezaei Letter to Editor 05 February 2019 Pages: 127 - 130
Compound Heterozygous Mutations of IL2-Inducible T cell Kinase in a Swedish Patient: the Importance of Early Genetic Diagnosis Mingyan FangHassan AbolhassaniLennart Hammarström Letter to Editor 12 February 2019 Pages: 131 - 134
IFN-g:IL-10 Ratio: a Putative Predictive Biomarker to Discriminate HLH From Severe Viral Infections Snehal ShabrishMukesh DesaiManisha Madkaikar Letter to Editor 19 February 2019 Pages: 135 - 137
Auto-inflammation in a Patient with a Novel Homozygous OTULIN Mutation Mohammad NabaviMohammad ShahrooeiXavier Bossuyt Letter 22 February 2019 Pages: 138 - 141
In Memoriam: Fernando Aiuti, MD (June 8, 1935–January 9, 2019) Alessandro AiutiIsabella Quinti Letter to Editor 05 March 2019 Pages: 142 - 143
A Novel FOXN1 Variant Is Identified in Two Siblings with Nude Severe Combined Immunodeficiency Sinem FirtinaFunda CipeMuge Sayitoglu Letter to Editor 22 March 2019 Pages: 144 - 147
Immune Dysregulation and Disease Pathogenesis due to Activating Mutations in PIK3CD—the Goldilocks’ Effect Stuart G. TangyeJulia BierElissa K. Deenick CME Review 25 March 2019 Pages: 148 - 158
Health-Related Quality of Life in Patients with CVID Under Different Schedules of Immunoglobulin Administration: Prospective Multicenter Study Federica PulvirentiFrancesco CinettoCinzia Milito Original Article Open access 15 January 2019 Pages: 159 - 170
Neurological Involvement in Childhood Evans Syndrome Thomas PincezBénédicte NevenNathalie Aladjidi Original Article 22 January 2019 Pages: 171 - 181
Haploidentical Stem Cell Transplantation with Post-Transplant Cyclophosphamide for Primary Immune Deficiency Disorders in Children: Challenges and Outcome from a Tertiary Care Center in South India Ramya UppuluriMeena SivasankaranRevathi Raj Original Article 18 February 2019 Pages: 182 - 187
Novel Heterogeneous Mutation of TNFAIP3 in a Chinese Patient with Behçet-Like Phenotype and Persistent EBV Viremia Xiaolong DongLuyao LiuXiaochuan Wang Original Article 27 February 2019 Pages: 188 - 194
Health-Related Quality of Life and Emotional Health in X-Linked Carriers of Chronic Granulomatous Disease in the United Kingdom Alexandra C. BattersbyHelen BragginsAndrew R. Gennery Original Article Open access 13 March 2019 Pages: 195 - 199
Severe Transitory Neonatal Neutropenia Associated with Maternal Autoimmune or Idiopathic Neutropenia Julie SeguierVincent BarlogisNicolas Schleinitz Original Article 21 March 2019 Pages: 200 - 206
Alternative Splicing Rescues Loss of Common Gamma Chain Function and Results in IL-21R-like Deficiency David IlligMarta NavratilDaniel Kotlarz Original Article 21 March 2019 Pages: 207 - 215
Nasal Nitric Oxide in Primary Immunodeficiency and Primary Ciliary Dyskinesia: Helping to Distinguish Between Clinically Similar Diseases Zofia N. Zysman-ColmanKimberley R. KaspyAdam J. Shapiro Original Article 26 March 2019 Pages: 216 - 224
Correction to: Imaging of Bronchial Pathology in Antibody Deficiency: Data from the European Chest CT Group Katharina SchützDiana Alecsandrufor the Chest CT in Antibody Deficiency Group Correction 23 March 2019 Pages: 225 - 227