IKBA S32 Mutations Underlie Ectodermal Dysplasia with Immunodeficiency and Severe Noninfectious Systemic Inflammation Kunihiko MoriyaYoji SasaharaHirokazu Kanegane Letter to Editor 14 June 2018 Pages: 543 - 545
Severe Congenital Neutropenia associated with SRP54 mutation in 22q11.2 Deletion Syndrome: Hematopoietic Stem Cell Transplantation Results in Correction of Neutropenia with Adequate Immune Reconstitution Marcus A. CardenJames A. ConnellyShanmuganathan Chandrakasan Letter to Editor 29 June 2018 Pages: 546 - 549
Reflex Testing of Immunoglobulins in Patients with Total Serum IgE < 2 kU/L Lisa CampisiTamara ForsterMohammed Yousuf Karim Letter to Editor 29 June 2018 Pages: 550 - 552
Transient Marked Increase of γδ T Cells in WHIM Syndrome After Successful HSCT Yuta KawaharaYukiko OhAkira Morimoto Letter to Editor 04 July 2018 Pages: 553 - 555
Renal Disease in Chronic Granulomatous Disease: Data from the USIDNET Registry Keith A. SaccoElizabeth GarabedianAvni Y. Joshi Letter to Editor 05 July 2018 Pages: 556 - 557
The Autoimmune Lymphoproliferative Syndrome with Defective FAS or FAS-Ligand Functions Frédéric Rieux-LaucatAude Magérus-ChatinetBénédicte Neven CME Review 17 June 2018 Pages: 558 - 568
Deficiency of Adenosine Deaminase 2 (DADA2): Updates on the Phenotype, Genetics, Pathogenesis, and Treatment Isabelle MeytsIvona Aksentijevich CME Review Open access 27 June 2018 Pages: 569 - 578
The Treatment of Inflammatory Bowel Disease in Patients with Selected Primary Immunodeficiencies Dror S. ShouvalMatthew KowalikScott B. Snapper How I Manage 29 June 2018 Pages: 579 - 588
Utility of Ruxolitinib in a Child with Chronic Mucocutaneous Candidiasis Caused by a Novel STAT1 Gain-of-Function Mutation Markéta BloomfieldVeronika KanderováAnna Šedivá Original Article 22 June 2018 Pages: 589 - 601
Biweekly Hizentra® in Primary Immunodeficiency: a Multicenter, Observational Cohort Study (IBIS) Alessandra VultaggioChiara AzzariAndrea Matucci Original Article Open access 28 June 2018 Pages: 602 - 609
Clearing Vaccine-Derived Poliovirus Infection Following Hematopoietic Stem Cell Transplantation: a Case Report and Review of Literature Mohammadreza ShaghaghiMona IrannejadAsghar Aghamohammadi Original Article 14 June 2018 Pages: 610 - 616
A Variety of Alu-Mediated Copy Number Variations Can Underlie IL-12Rβ1 Deficiency Jérémie RosainCarmen Oleaga-QuintasJacinta Bustamante Original Article 11 July 2018 Pages: 617 - 627
Low Rates of Poliovirus Antibodies in Primary Immunodeficiency Patients on Regular Intravenous Immunoglobulin Treatment Beatriz T. Costa-CarvalhoKathleen E. SullivanMaria Isabel de Moraes-Pinto Original Article 14 July 2018 Pages: 628 - 634