The Expanding Spectrum of NFkB1 Deficiency Vanessa L. BryantStuart G. Tangye Editorial 23 June 2016 Pages: 531 - 532
NF-κB1 Haploinsufficiency Causing Immunodeficiency and EBV-Driven Lymphoproliferation Heidrun BoztugTatjana HirschmuglKaan Boztug ORIGINAL ARTICLE Open access 23 June 2016 Pages: 533 - 540
A Novel Mutation in IKBKG/NEMO Leads to Ectodermal Dysplasia with Severe Immunodeficiency (EDA-ID) Alicia M. JohnstonJulie NiemelaHyesun Kuehn Letter to Editor 02 July 2016 Pages: 541 - 543
Activated PI3-kinase δ Syndrome: Long-term Follow-up after Cord Blood Transplantation Antony CerauloChristophe MalcusYves Bertrand Letter to Editor 13 June 2016 Pages: 544 - 546
A Founder Effect of c.257 + 2T > C Mutation in NCF2 Gene Underlies Severe Chronic Granulomatous Disease in Eleven Patients Khaoula Ben-FarhatImen Ben-MustaphaMohamed-Ridha Barbouche Original Article 25 May 2016 Pages: 547 - 554
Expanded CD4+ Effector/Memory T Cell Subset in APECED Produces Predominantly Interferon Gamma Nelli HeikkiläSini M. LaaksoTommi P. Arstila Original Article 04 June 2016 Pages: 555 - 563
X-linked Hyper IgM Syndrome Presenting as Pulmonary Alveolar Proteinosis Joel GallagherJuan AdamsJohn Routes Original Article 20 June 2016 Pages: 564 - 570
Long-Term Tolerability, Safety, and Efficacy of Recombinant Human Hyaluronidase-Facilitated Subcutaneous Infusion of Human Immunoglobulin for Primary Immunodeficiency Richard L. WassermanIsaac MelamedDavid Gelmont Original Article Open access 25 May 2016 Pages: 571 - 582
Flebogamma® 5 % DIF Intravenous Immunoglobulin for Replacement Therapy in Children with Primary Immunodeficiency Diseases Mark BallowPaul J. PinciaroWilliam Smits Original Article 08 June 2016 Pages: 583 - 589
Efficacy, Safety, and Pharmacokinetics of a New 10 % Liquid Intravenous Immunoglobulin Containing High Titer Neutralizing Antibody to RSV and Other Respiratory Viruses in Subjects with Primary Immunodeficiency Disease Richard L. WassermanWilliam LumryRoger Kobayashi Original Article Open access 20 June 2016 Pages: 590 - 599
Pharmacokinetics, Safety, and Tolerability of Subcutaneous Immune Globulin Injection (Human), 10 % Caprylate/Chromatography Purified (GAMUNEX®-C) in Pediatric Patients with Primary Immunodeficiency Disease Jennifer HeimallJunliang ChenGary I. Kleiner Original Article 25 June 2016 Pages: 600 - 609
Role of Flow Cytometry in the Diagnosis of Chronic Granulomatous Disease: the Egyptian Experience Rabab El HawarySafa MeshaalAisha Elmarsafy Original Article 24 May 2016 Pages: 610 - 618