“Good’s Syndrome Presenting with Recurrent Giardiasis” Amit RawatVarun DhirSurjit Singh Letter to Editor 22 July 2014 Pages: 751 - 752
Inborn errors of metabolism underlying primary immunodeficiencies Nima ParvanehPierre QuartierPascale de Lonlay Key Review Article 01 August 2014 Pages: 753 - 771
XLP: Clinical Features and Molecular Etiology due to Mutations in SH2D1A Encoding SAP Stuart G Tangye Key Review Article 02 August 2014 Pages: 772 - 779
Clinical Course in a Patient With Neutrophil-Specific Granule Deficiency and Rapid Detection of Neutrophil Granules as a Screening Test Tomonari ShigemuraTakashi YamazakiKazunaga Agematsu Astute Clinician Report 01 August 2014 Pages: 780 - 783
A Novel Treatment in X-Linked Agammaglobulinaemia - Hyperbaric Oxygen Therapy in Refractory Chronic Wounds C. L. SteeleC. CridgeJ. D. M. Edgar Astute Clinician Report 05 August 2014 Pages: 784 - 787
Successful Anti-TNF-α Treatment in a Girl with LAD-1 Disease and Autoimmune Manifestations Manuela MarsiliVassilios LougarisLuciana Breda Astute Clinician Report 19 August 2014 Pages: 788 - 791
Atypical Severe Combined Immunodeficiency Caused by a Novel Homozygous Mutation In Rag1 Gene in a Girl who Presented with Pyoderma Gangrenosum: A Case Report and Literature Review Turkan PatirogluH. Haluk AkarEkrem Unal Astute Clinician Report 08 August 2014 Pages: 792 - 795
Identification of Germinal Centres in the Lymph Node of a Patient with Hyperimmunoglobulin M Syndrome Associated with Congenital Rubella Rohan AmeratungaChun-Jen J. ChenSee-Tarn Woon Original Research 12 August 2014 Pages: 796 - 803
Clinical Experience With an L-Proline–Stabilized 10 % Intravenous Immunoglobulin (Privigen®): Real-Life Effectiveness and Tolerability Morna J. DorseyViet HoMelvin Berger Original Research Open access 01 July 2014 Pages: 804 - 812
Adequate Patient’s Outcome Achieved with Short Immunoglobulin Replacement Intervals in Severe Antibody Deficiencies Cinzia MilitoFederica PulvirentiIsabella Quinti Original Research Open access 22 July 2014 Pages: 813 - 819
Infliximab for Treatment of Granulomatous Disease in Patients with Common Variable Immunodeficiency Timothy J. FranxmanLaura E. HoweJames R. Baker Jr. Original Research 27 July 2014 Pages: 820 - 827
Optimal Strategies to Identify Aberrant Intra-Epithelial Lymphocytes in Refractory Coeliac Disease R. L. J. van WanrooijD. M. J. MüllerC. J. J. Mulder Original Research 27 July 2014 Pages: 828 - 835
Primary Immunodeficiency Diseases: A 30-year Patient Registry from the Referral Center for Primary Immunodeficiencies in Greece Athanasios MichosMaria RaptakiMaria Kanariou Original Research 01 July 2014 Pages: 836 - 843
Quality of Life in Children with Primary Antibody Deficiency P. TitmanZ. AllwoodA. Jones Original Research Open access 09 July 2014 Pages: 844 - 852
IgA Deficiency, Autoimmunity & Pregnancy: A Population-Based Matched Cohort Study Jonas F LudvigssonMartin NeoviusLennart Hammarström Original Research 09 July 2014 Pages: 853 - 863
Helios Expression in T-regulatory Cells in Patients with di George Syndrome Adam KlocperkJarmila GrecováAnna Šedivá Original Research 10 July 2014 Pages: 864 - 870
Compound Heterozygous CORO1A Mutations in Siblings with a Mucocutaneous-Immunodeficiency Syndrome of Epidermodysplasia Verruciformis-HPV, Molluscum Contagiosum and Granulomatous Tuberculoid Leprosy Asbjorg Stray-PedersenEmmanuelle JouanguyLenora M. Noroski Original Research 30 July 2014 Pages: 871 - 890