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Periodische Fieberschübe und Pharyngitis bei Kindern

Das PFAPA-Syndrom: Tonsillektomie als Therapieoption!

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HNO Nachrichten Aims and scope

Das PFAPA-Syndrom ist eine seltene Erkrankung, die schon im frühen Kindesalter auftritt. Das Vollbild ist gekennzeichnet durch periodische Fieberschübe, begleitet von einer aphthösen Stomatitis, Pharyngitis und zervikalen Lymphadenitis. Neben der medikamentösen Therapie vor allem mit Steroiden beschreiben einige Publikationen ein komplettes Sistieren der Fieberschübe und der Symptomatik nach Tonsillektomie.

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  1. Renatastraße 71, 80639, München, Deutschland

    Richard de la Chaux (HNO-Praxis)

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de la Chaux, R. Das PFAPA-Syndrom: Tonsillektomie als Therapieoption!. HNO Nachrichten 48, 26–30 (2018). https://doi.org/10.1007/s00060-018-5643-7

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