Summary
The first case of congenital defect of the skull and scalp in Japan, probably due to an immature arteriovenous malformation, is presented. In this case, an island of healthy scalp remained intact in the central area of the scalp defect, unlike previously reported cases. The dilated, tortuous scalp vessels apparently disappeared spontaneously only after multiple ligation. Because of slow wound healing, three successive operations were subsequently needed to cover the scalp defect. The cause of the aplasia cutis congenita and the delayed wound healing mechanism was investigated histologically.
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Ohtsuka, H., Yamamoto, M. & Okayama, N. Aplasia cutis congenita associated with an immature arteriovenous malformation. Eur J Plast Surg 13, 268–271 (1990). https://doi.org/10.1007/BF00208330
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DOI: https://doi.org/10.1007/BF00208330