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Angeborene Anomalien des Pankreas

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SpringerReference Innere Medizin

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Zusammenfassung

Angeborene Pankreaszysten kommen sehr selten vor. Sie treten in der Regel solitär oder in Assoziation mit Nieren- oder Leberzysten sowie anderen angeborenen Erkrankungen auf. Das Pancreas divisum ist die häufigste kongenitale anatomische Anomalie des Pankreas. Es entsteht als sporadische Entwicklungsvariante des Pankreas aufgrund einer unvollständigen Fusion der ventralen mit der dorsalen Pankreasanlage. Als Folge dessen sind der Ductus Wirsungianus und der Ductus Santorini nicht (komplettes Pancreas divisum) oder nur unvollständig (inkomplettes Pancreas divisum) miteinander verbunden, sodass der Großteil des exokrinen Pankreassekrets durch die Minorpapille drainiert wird. Das Pancreas anulare ist eine seltene Entwicklungsstörung des Pankreas, bei der die Rotation der ventralen Pankreasanlage um das Duodenum unvollständig ist. Folge dessen ist ein ringförmig die Pars descendens duodeni umschließendes Pankreas. Das Pancreas bifidum ist eine sehr seltene Fusionsanomalie des Pankreas, bei der das Pankreas im Schwanzbereich einen zweigeteilten Hauptgang aufweist. Die seltene Pankreasektopie beschreibt das Vorhandensein von Pankreasgewebe an einer abnormalen Lokalisation.

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Authors and Affiliations

  1. Medizinische Klinik, Evangelisches Krankenhaus Düsseldorf, Kirchfeldstr. 40, 40217, Düsseldorf, Deutschland

    Jennis Kandler & Horst Neuhaus

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  1. Jennis Kandler
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  2. Horst Neuhaus
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Correspondence to Jennis Kandler .

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Editors and Affiliations

  1. Medizinische Klinik I, Universitätsklinikum Schleswig-Hoslstein, Campus Lübeck, Lübeck, Schleswig-Holstein, Germany

    Hendrik Lehnert

  2. TU Dresden Universitätsklinikum Carl Gustav Carus, Dresden, Germany

    Sebastian M. Schellong

  3. FB Gastroenterologie und Hepatologie, Universitätsklinikum Leipzig Medizinische Klinik und Poliklinik II, Leipzig, Sachsen, Germany

    Joachim Mössner

  4. Krankenhaus Barmherzige Brüder, Regensburg, Germany

    Cornel C. Sieber

  5. Nürnberg, Bayern, Germany

    Walter Swoboda

  6. Universitätsklinikum Giessen und Marburg Klinik für Innere Medizin, Marburg, Hessen, Germany

    Andreas Neubauer

  7. Interdisziplinärer Schwerpunkt für Hämos, Universitätsklinikum Gießen und Marburg, Gießen, Germany

    Bettina Kemkes-Matthes

  8. Klinik für Gastroenterologie,Hepatologie, Medizinische Hochschule Hannover, Hannover, Germany

    Michael P. Manns

  9. Sektion für Molekulare und Klinische Inf, Universitätsklinikum Schleswig-Holstein,, Lübeck, Germany

    Jan Rupp

  10. Abt. Kardiologie und Pneumologie, Universitätsklinikum Göttingen Herzzentrum Göttingen, Göttingen, Germany

    Gerd Hasenfuß

  11. Abt. Nephrologie und Klinische Immunologie, Univ.Klinikum Aachen Medizinische Klinik II, Aachen, Germany

    J. Floege

  12. Universitätsklinikum Köln Klinik I für Innere Medizin, Köln, Germany

    Michael Hallek

  13. Klinik für Pneumologie, Medizinische Hochschule Hannover (MHH) Zentrum Innere Medizin, Hannover, Germany

    Tobias Welte

  14. Klinik u. Poliklinik für Innere Medizin, Universitätsmedizin Greifswald, Greifswald, Germany

    Markus Lerch

  15. Dr.-Horst-Schmidt-Kliniken GmbH, Wiesbaden, Germany

    Elisabeth Märker-Hermann

  16. Klinische Toxikologie, Giftinformation, Universitätsklinikum Mainz II. Medizinische Klinik und Poliklinik, Mainz, Germany

    Ludwig Sacha Weilemann

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Kandler, J., Neuhaus, H. (2015). Angeborene Anomalien des Pankreas. In: Lehnert, H., et al. SpringerReference Innere Medizin. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-54676-1_68-1

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