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Spinal Deformity in Metabolic Diseases

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The Growing Spine

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Abstract

Soft bone disease comes in many forms and may cause or coexist with spinal deformity. The poor bone quality may cause macrofractures or microfractures or plastic bone deformation creating a spinal deformity. Bracing is typically ineffective and the pressure from bracing creates secondary deformities of the chest wall. Surgery is complicated by the soft bone, which makes correction difficult from poor bone purchase and which bleeds if fractured. There are several strategies to minimize these problems, but some appear unavoidable with current knowledge and techniques. This chapter outlines some generalities that are discussed in more detail with the specific diseases.

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Authors and Affiliations

  1. Department of Orthopaedics and Rehabilitation, University of Rochester, 601 Elmwood Avenue, Rochester, NY, 14642, USA

    James O. Sanders

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  1. James O. Sanders
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  2. Kerry Armet
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  3. Susan Bukata
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Editors and Affiliations

  1. Orthopaedic Surgery, San Diego Medical Director, San Diego Center for Spinal Disorders, University of California, 4130 La Jolla, Village Drive, La Jolla, CA, 92037, USA

    Behrooz A. Akbarnia MD

  2. Orthopaedic Surgery Department of Orthopaedics & Traumatology, Hacettepe University, 06100 Sihhiye, Ankara, Turkey

    Muharrem Yazici MD

  3. Pediatric Orthopaedics Rainbow Babies & Children’s Hospital, Case Western Reserve University, 11000 Euclid Avenue, Cleveland, OH, 44106-6003, USA

    George H. Thompson MD

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Sanders, J.O., Armet, K., Bukata, S. (2011). Spinal Deformity in Metabolic Diseases. In: Akbarnia, B.A., Yazici, M., Thompson, G.H. (eds) The Growing Spine. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-85207-0_14

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  • DOI: https://doi.org/10.1007/978-3-540-85207-0_14

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