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Cardiomyopathies

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Abstract

In 1995, the World Health Organization (WHO) defined five classes of cardiomyopathies: Dilated cardiomyopathy (DCM), hypertrophic cardiomyopathy (HCM), restrictive cardiomyopathy, arrhythmogenic right ventricular cardiomyopathy (ARVC), and unclassified cardiomyopathies. According to the more recent scientific statement on “contemporary definitions and classification of the cardiomyopathies” published in 2006 by the American Heart Association (AHA)1, cardiomyopathies are “a heterogeneous group of diseases of the myocardium associated with mechanical and/or electrical dysfunction that usually (but not invariably) exhibit inappropriate ventricular hypertrophy or dilatation and are due to a variety of causes that frequently are genetic. Cardiomyopathies either are confined to the heart or are part of generalized systemic disorders, often leading to cardiovascular death or progressive heart failure–related disability.” This new definition acknowledges the wide range of myocardial diseases, some of which are primary (predominantly involving the myocardium), others secondary (due to a systemic disease affecting other organs).

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© 2010 Springer-Verlag London Limited

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Plein, S., Greenwood, J.P., Ridgway, J.P. (2010). Cardiomyopathies. In: Cardiovascular MR Manual. Springer, London. https://doi.org/10.1007/978-1-84996-362-6_23

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  • DOI: https://doi.org/10.1007/978-1-84996-362-6_23

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  • Publisher Name: Springer, London

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