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Chronic Thromboembolic Pulmonary Hypertension

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Diagnosis and Management of Pulmonary Hypertension

Part of the book series: Respiratory Medicine ((RM,volume 12))

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Abstract

Chronic thromboembolic pulmonary hypertension (CTEPH) is a potential outcome in approximately 1–4 % of patients having experienced one or more acute pulmonary embolic events. Despite this recognized complication of acute thromboembolic disease, this clinical entity remains underdiagnosed. The importance of diagnosing CTEPH in any pulmonary hypertensive patient centers on the realization that, with surgical thromboendarterectomy, a potential cure for this form of pulmonary hypertension is currently available. For those patients with inoperable chronic thromboembolic pulmonary hypertension, recent advances in the development of pulmonary hypertensive specific medical therapy now offer hope for an improvement in pulmonary hemodynamics and functional status. This chapter presents an updated review of the epidemiology, pathophysiology, clinical presentation, assessment, and treatment options for those patients with chronic thromboembolic pulmonary hypertension.

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Authors and Affiliations

  1. Division of Pulmonary and Critical Care Medicine, University of California, San Diego, 9300 Campus Point Drive, La Jolla, CA, 92037, USA

    William R. Auger M.D. & Peter F. Fedullo M.D.

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  1. William R. Auger M.D.
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  2. Peter F. Fedullo M.D.
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Correspondence to William R. Auger M.D. .

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  1. Division of Pulmonary, Sleep and Critical Care Medicine, Rhode Island Hospital, Alpert Medical School of Brown University, Providence, Rhode Island, USA

    James R. Klinger

  2. Department of Medicine, Mayo Clinic College of Medicine, Rochester, Minnesota, USA

    Robert P. Frantz

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Auger, W.R., Fedullo, P.F. (2015). Chronic Thromboembolic Pulmonary Hypertension. In: Klinger, J., Frantz, R. (eds) Diagnosis and Management of Pulmonary Hypertension. Respiratory Medicine, vol 12. Humana Press, New York, NY. https://doi.org/10.1007/978-1-4939-2636-7_6

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