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Sialidase in Brain and Fibroblasts in Three Patients with Different Types of Sialidosis

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Book cover Structure and Function of Gangliosides

Part of the book series: Advances in Experimental Medicine and Biology ((AEMB,volume 125))

Abstract

In recent years numerous diseases have become known which are characterized by an elevated urinary excretion of sialooligosaccharides and a deficiency of sialidase in cultured fibroblasts (for literature, see SPRANGER, GEHLER and CANTZ, 1977; STRECKER and MICHALSKI, 1978; MAROTEAUX, 1978).

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Author information

Authors and Affiliations

  1. Neurochemische Abteilung, Max-Planck-Institut für Psychiatrie, 8000, München 40, Germany

    Bernhard Pallmann & Konrad Sandhoff

  2. College of Pharmacy, University of Milan, Italy

    Bruno Berra (Chair of Biochemistry)

  3. Department of Neurology, Jichi Medical School, Yakushiji, Tochigi, Japan

    Tadashi Miyatake

Authors
  1. Bernhard Pallmann
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  2. Konrad Sandhoff
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  3. Bruno Berra
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  4. Tadashi Miyatake
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Editor information

Editors and Affiliations

  1. Psychiatric Research Centre, Department of Neurochemistry, St. Jörgen Hospital, Göteborg, Sweden

    Lars Svennerholm

  2. C. N. R. S. Center for Neurochemistry, Strasbourg, France

    Paul Mandel , Henri Dreyfus  & Paul-Francis Urban ,  & 

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© 1980 Plenum Press, New York

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Pallmann, B., Sandhoff, K., Berra, B., Miyatake, T. (1980). Sialidase in Brain and Fibroblasts in Three Patients with Different Types of Sialidosis. In: Svennerholm, L., Mandel, P., Dreyfus, H., Urban, PF. (eds) Structure and Function of Gangliosides. Advances in Experimental Medicine and Biology, vol 125. Springer, Boston, MA. https://doi.org/10.1007/978-1-4684-7844-0_37

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  • DOI: https://doi.org/10.1007/978-1-4684-7844-0_37

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4684-7846-4

  • Online ISBN: 978-1-4684-7844-0

  • eBook Packages: Springer Book Archive

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