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Arthrogryposis

Upper Extremity Reconstruction for Arthrogryposis

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Abstract

The care of the child with arthrogryposis requires a global understanding of that child’s needs and abilities. The results of any intervention at one joint in the arm can be influenced not only by the condition of other joints in that limb, but in the lower extremities as well. Treatment options at the shoulder are limited, with a humeral rotational osteotomy performed most commonly to address an internal rotation contracture. The elbow is most often positioned in extension, often requiring a posterior capsular release with triceps lengthening and ulnar nerve transposition to gain passive motion. Active elbow flexion is more difficult to achieve. At the wrist, the carpal wedge osteotomy has recently been shown to have reliably good results in correcting wrist flexion contractures (J Bone Joint Surg Am. 2013;95(20):e150; J Hand Surg Am. 2013;38(2):265–70). Correction of thumb deformities can reliably improve pinch and grasp, while correction of camptodactyly remains unpredictable.

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Correspondence to Dan A. Zlotolow .

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© 2015 Springer Science+Business Media New York

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Zlotolow, D.A., Kozin, S.H. (2015). Arthrogryposis. In: Abzug, J., Kozin, S., Zlotolow, D. (eds) The Pediatric Upper Extremity. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-8515-5_35

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  • DOI: https://doi.org/10.1007/978-1-4614-8515-5_35

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  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4614-8513-1

  • Online ISBN: 978-1-4614-8515-5

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