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Is There a Role for TEVAR in Marfan’s Syndrome?

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Controversies in Aortic Dissection and Aneurysmal Disease

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Abstract

Over the last decades, the remarkable improvement of medical and surgical therapy has dramatically increased expectancy of life in Marfan patients. As a result, the number of such patients requiring secondary interventions on the descending thoracic aorta or thoraco-abdominal aorta due to new or residual dissections, rupture and distal aneurysm formation has substantially enlarged. Surgical and endovascular procedures represent two valuable options of treatment, both associated with advantages and drawbacks. Aim of the present chapter was to review surgical and endovascular outcomes in Marfan patients in order to identify a potential role of TEVAR in this context.

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Author information

Authors and Affiliations

  1. Interventional Cardiology Unit, San Salvatore Hospital, Ospedale San Salvatore, Piazza Cinelli 4, Pesaro, 61121, Italy

    Rossella Fattori

  2. Cardiovascular Department, Cardiac Surgery, Alma Mater Studiorum Università di Bologna, Policlinico S. Orsola-Malpaghini Hospital, Via Massarenti, 9, Bologna, 40318, Italy

    Marco Di Eusanio MD, PhD

  3. Cardiac Surgery Department, Policlinico Sant’Orsola-Malpighi, University of Bologna, Bologna, Italy

    Marco Di Eusanio MD, PhD

Authors
  1. Rossella Fattori
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  2. Marco Di Eusanio MD, PhD
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Corresponding author

Correspondence to Marco Di Eusanio MD, PhD .

Editor information

Editors and Affiliations

  1. University Hospitals Birmingham, Queen Elizabeth Hospital, Birmingham, United Kingdom

    Robert S. Bonser

  2. University Hospitals Birmingham, Queen Elizabeth Hospital, Birmingham, United Kingdom

    Domenico Pagano

  3. Thoracic and Cardiovascular Surgery Depts., Hannover Medical School, Hannover, Germany

    Axel Haverich

  4. University Hospitals Birmingham, Queen Elizabeth Hospital & Centre, Birmingham, United Kingdom

    Jorge Mascaro

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© 2014 Springer-Verlag London

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Fattori, R., Di Eusanio, M. (2014). Is There a Role for TEVAR in Marfan’s Syndrome?. In: Bonser, R., Pagano, D., Haverich, A., Mascaro, J. (eds) Controversies in Aortic Dissection and Aneurysmal Disease. Springer, London. https://doi.org/10.1007/978-1-4471-5622-2_38

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  • DOI: https://doi.org/10.1007/978-1-4471-5622-2_38

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-5621-5

  • Online ISBN: 978-1-4471-5622-2

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