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Sydenham’s Chorea, PANDAS, and Other Poststreptococcal Neurological Disorders

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Movement Disorder Emergencies

Part of the book series: Current Clinical Neurology ((CCNEU))

Abstract

A 12-year-old boy developed hyperthyroidism secondary to Grave’s disease, which was successfully treated with I-131 treatment. Several months later, pharyngeal infection with group A β-hemolytic Streptococcus was documented by throat culture and subsequent rise in antistreptolysin O titer. He was treated with oral antibiotics, and 2 weeks later developed insidious, progressive chorea, incoordination with right hemibody, and imbalance. Examination revealed moderate chorea affecting the eyes, arms, and legs, incoordination of fine hand movements, motor impersistence on hand grip and tongue protrusion, and near inability to walk. He was treated with valproic acid, and his symptoms resolved within 3 weeks.

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Authors and Affiliations

  1. Department of Neurology, Columbia University Medical Center, New York, NY

    Roser Pons MD

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  1. Roser Pons MD
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© 2005 Humana Press Inc.

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Pons, R. (2005). Sydenham’s Chorea, PANDAS, and Other Poststreptococcal Neurological Disorders. In: Movement Disorder Emergencies. Current Clinical Neurology. Humana Press. https://doi.org/10.1385/1-59259-902-8:135

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  • DOI: https://doi.org/10.1385/1-59259-902-8:135

  • Publisher Name: Humana Press

  • Print ISBN: 978-1-58829-305-3

  • Online ISBN: 978-1-59259-902-8

  • eBook Packages: MedicineMedicine (R0)

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