Abstract
Pathologists, clinicians, and radiologists have traditionally confused the diagnosis of vascular anomalies. The International Society for the Study of Vascular Anomalies (ISSVA) advocated a classification that divided vascular anomalies into the following two major categories: tumors and malformations. This classification system is now widely accepted for properly diagnosing and treating vascular anomalies (Sepulveda and Buchanan 2014; Lowe et al. 2012). According to this classification system, vascular tumors (except congenital hemangiomas) are endothelial neoplasms that grow via endothelial hyperplasia, are not clinically present at birth, have a period of rapid growth, and spontaneously involute (except noninvoluting congenital hemangiomas). Vascular malformations are composed of capillaries, veins, lymphatics, and/or arteries with normal endothelial cell turnover, are present at birth, and grow proportionally with the child. However, vascular tumors will be the focus of this chapter, based on 2013 WHO classification of soft tissue tumors.
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Kang, H.S., Hong, S.H., Choi, JY., Yoo, H.J. (2017). Vascular Tumors. In: Oncologic Imaging: Soft Tissue Tumors. Springer, Singapore. https://doi.org/10.1007/978-981-287-718-5_10
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