Surgical Management of Total Colonic Aganglionosis and Extensive Aganglionosis

  • Yutaka KanamoriEmail author


Total colonic aganglionosis (TCA) is a rare form of Hirschsprung disease and is defined as aganglionosis extending to the cecum or distal ileum. The mortality rate of this disease declined dramatically recently, but the morbidity rate is still high. Although several operative procedures have been adopted for TCA such as Martin, Duhamel, Soave, Swenson, and colon patch, with some modifications, the optimal procedure is not apparent, and we need to develop a novel treatment strategy to improve the high morbidity rate after pull-through operation.


Total colonic aganglionosis Extensive aganglionosis Martin method 


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Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  1. 1.Division of Surgery, Department of Surgical SpecialtiesNational Center for Child Health and DevelopmentTokyoJapan

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